ICD-10-CM/PCS MS-DRG v41.1 Definitions Manual
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Appendix C: Principal diagnoses which convert CC/MCC to non-CC
Page 62 of 429
PDX Collection 0611 (continued)
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71518Other disorders of peroxisome biogenesis
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0612
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71520Childhood cerebral X-linked adrenoleukodystrophy
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0613
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71521Adolescent X-linked adrenoleukodystrophy
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0614
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71522Adrenomyeloneuropathy
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0615
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71528Other X-linked adrenoleukodystrophy
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0616
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71529X-linked adrenoleukodystrophy, unspecified type
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0617
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E7153Other group 2 peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0618
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71540Rhizomelic chondrodysplasia punctata
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0619
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71541Zellweger-like syndrome
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0620
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71542Other group 3 peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0621
C965Multifocal and unisystemic Langerhans-cell histiocytosis
C966Unifocal Langerhans-cell histiocytosis
E71310Long chain/very long chain acyl CoA dehydrogenase deficiency
E71311Medium chain acyl CoA dehydrogenase deficiency
E71312Short chain acyl CoA dehydrogenase deficiency
E71313Glutaric aciduria type II
E71314Muscle carnitine palmitoyltransferase deficiency
E71318Other disorders of fatty-acid oxidation
E7132Disorders of ketone metabolism
E7139Other disorders of fatty-acid metabolism
E7140Disorder of carnitine metabolism, unspecified
E7141Primary carnitine deficiency
E7142Carnitine deficiency due to inborn errors of metabolism
E7143Iatrogenic carnitine deficiency
E71440Ruvalcaba-Myhre-Smith syndrome
E71448Other secondary carnitine deficiency
E71548Other peroxisomal disorders
E803Defects of catalase and peroxidase
E804Gilbert syndrome
E805Crigler-Najjar syndrome
E806Other disorders of bilirubin metabolism
E807Disorder of bilirubin metabolism, unspecified
E8840Mitochondrial metabolism disorder, unspecified
E8841MELAS syndrome
E8842MERRF syndrome
E8843Disorders of mitochondrial tRNA synthetases
E8849Other mitochondrial metabolism disorders
E88811Insulin resistance syndrome, Type A
E88818Other insulin resistance
E88819Insulin resistance, unspecified
E8889Other specified metabolic disorders
H49811Kearns-Sayre syndrome, right eye
H49812Kearns-Sayre syndrome, left eye
H49813Kearns-Sayre syndrome, bilateral
H49819Kearns-Sayre syndrome, unspecified eye
 
PDX Collection 0622
E7203Lowe's syndrome
 
PDX Collection 0623
C880Waldenstrom macroglobulinemia
D472Monoclonal gammopathy
D890Polyclonal hypergammaglobulinemia
D891Cryoglobulinemia
E700Classical phenylketonuria
E701Other hyperphenylalaninemias
E7020Disorder of tyrosine metabolism, unspecified
E7021Tyrosinemia
E7029Other disorders of tyrosine metabolism
E7030Albinism, unspecified
E70310X-linked ocular albinism
E70311Autosomal recessive ocular albinism
E70318Other ocular albinism
E70319Ocular albinism, unspecified
E70320Tyrosinase negative oculocutaneous albinism
E70321Tyrosinase positive oculocutaneous albinism
E70328Other oculocutaneous albinism
E70329Oculocutaneous albinism, unspecified
E70330Chediak-Higashi syndrome
E70331Hermansky-Pudlak syndrome
E70338Other albinism with hematologic abnormality
E70339Albinism with hematologic abnormality, unspecified
E7039Other specified albinism
E7040Disorders of histidine metabolism, unspecified



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