| Dx | CC/MCC | Exclusions | Description |
| O98812 | CC | 1013:36 codes | Other maternal infectious and parasitic diseases complicating pregnancy, second trimester |
| O98813 | CC | 1013:36 codes | Other maternal infectious and parasitic diseases complicating pregnancy, third trimester |
| O9882 | CC | 1013:36 codes | Other maternal infectious and parasitic diseases complicating childbirth |
| O9883 | CC | 1013:36 codes | Other maternal infectious and parasitic diseases complicating the puerperium |
| O98911 | CC | 1013:36 codes | Unspecified maternal infectious and parasitic disease complicating pregnancy, first trimester |
| O98912 | CC | 1013:36 codes | Unspecified maternal infectious and parasitic disease complicating pregnancy, second trimester |
| O98913 | CC | 1013:36 codes | Unspecified maternal infectious and parasitic disease complicating pregnancy, third trimester |
| O9892 | CC | 1013:36 codes | Unspecified maternal infectious and parasitic disease complicating childbirth |
| O9893 | CC | 1013:36 codes | Unspecified maternal infectious and parasitic disease complicating the puerperium |
| O99111 | CC | 1016:53 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, first trimester |
| O99112 | CC | 1016:53 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, second trimester |
| O99113 | CC | 1016:53 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, third trimester |
| O99119 | CC | 1017:10 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, unspecified trimester |
| O9912 | CC | 1016:53 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating childbirth |
| O9913 | CC | 1016:53 codes | Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating the puerperium |
| O99321 | CC | 1018:229 codes | Drug use complicating pregnancy, first trimester |
| O99322 | CC | 1018:229 codes | Drug use complicating pregnancy, second trimester |
| O99323 | CC | 1018:229 codes | Drug use complicating pregnancy, third trimester |
| O99324 | CC | 1018:229 codes | Drug use complicating childbirth |
| O99325 | CC | 1018:229 codes | Drug use complicating the puerperium |
| O99354 | CC | 1016:53 codes | Diseases of the nervous system complicating childbirth |
| O99355 | CC | 1016:53 codes | Diseases of the nervous system complicating the puerperium |
| O99411 | CC | 1019:230 codes | Diseases of the circulatory system complicating pregnancy, first trimester |
| O99412 | CC | 1019:230 codes | Diseases of the circulatory system complicating pregnancy, second trimester |
| O99413 | CC | 1019:230 codes | Diseases of the circulatory system complicating pregnancy, third trimester |
| O9942 | MCC | 1008:230 codes | Diseases of the circulatory system complicating childbirth |
| O9943 | CC | 1019:230 codes | Diseases of the circulatory system complicating the puerperium |
| O99830 | CC | 1013:36 codes | Other infection carrier state complicating pregnancy |
| O99834 | CC | 1013:36 codes | Other infection carrier state complicating childbirth |
| O99835 | CC | 1013:36 codes | Other infection carrier state complicating the puerperium |
| P100 | MCC | 1020:39 codes | Subdural hemorrhage due to birth injury |
| P101 | MCC | 1020:39 codes | Cerebral hemorrhage due to birth injury |
| P102 | CC | 1021:48 codes | Intraventricular hemorrhage due to birth injury |
| P103 | MCC | 1022:49 codes | Subarachnoid hemorrhage due to birth injury |
| P104 | MCC | 1020:39 codes | Tentorial tear due to birth injury |
| P108 | MCC | 1020:39 codes | Other intracranial lacerations and hemorrhages due to birth injury |
| P109 | MCC | 1020:39 codes | Unspecified intracranial laceration and hemorrhage due to birth injury |
| P110 | MCC | 1020:39 codes | Cerebral edema due to birth injury |
| P112 | MCC | 1020:39 codes | Unspecified brain damage due to birth injury |
| P119 | MCC | 1020:39 codes | Birth injury to central nervous system, unspecified |
| P122 | CC | 1023:40 codes | Epicranial subaponeurotic hemorrhage due to birth injury |
| P220 | MCC | 0748:70 codes | Respiratory distress syndrome of newborn |
| P230 | MCC | 0748:70 codes | Congenital pneumonia due to viral agent |
| P231 | MCC | 0748:70 codes | Congenital pneumonia due to Chlamydia |
| P232 | MCC | 0748:70 codes | Congenital pneumonia due to staphylococcus |
| P233 | MCC | 0748:70 codes | Congenital pneumonia due to streptococcus, group B |
| P234 | MCC | 0748:70 codes | Congenital pneumonia due to Escherichia coli |
| P235 | MCC | 0748:70 codes | Congenital pneumonia due to Pseudomonas |
| P236 | MCC | 0748:70 codes | Congenital pneumonia due to other bacterial agents |
| P238 | MCC | 0748:70 codes | Congenital pneumonia due to other organisms |
| P239 | MCC | 0748:70 codes | Congenital pneumonia, unspecified |
| P2401 | MCC | 0748:70 codes | Meconium aspiration with respiratory symptoms |
| P2411 | MCC | 0748:70 codes | Neonatal aspiration of (clear) amniotic fluid and mucus with respiratory symptoms |
| P2421 | MCC | 0748:70 codes | Neonatal aspiration of blood with respiratory symptoms |
| P2431 | MCC | 0748:70 codes | Neonatal aspiration of milk and regurgitated food with respiratory symptoms |
| P2481 | MCC | 0748:70 codes | Other neonatal aspiration with respiratory symptoms |
| P250 | MCC | 0748:70 codes | Interstitial emphysema originating in the perinatal period |
| P251 | MCC | 0748:70 codes | Pneumothorax originating in the perinatal period |
| P252 | MCC | 0748:70 codes | Pneumomediastinum originating in the perinatal period |
| P253 | MCC | 0748:70 codes | Pneumopericardium originating in the perinatal period |
| P258 | MCC | 0748:70 codes | Other conditions related to interstitial emphysema originating in the perinatal period |
| P260 | MCC | 0748:70 codes | Tracheobronchial hemorrhage originating in the perinatal period |
| P261 | MCC | 0748:70 codes | Massive pulmonary hemorrhage originating in the perinatal period |
| P268 | MCC | 0748:70 codes | Other pulmonary hemorrhages originating in the perinatal period |
| P269 | MCC | 0748:70 codes | Unspecified pulmonary hemorrhage originating in the perinatal period |
| P270 | MCC | 0748:70 codes | Wilson-Mikity syndrome |
| P271 | MCC | 0748:70 codes | Bronchopulmonary dysplasia originating in the perinatal period |
| P278 | MCC | 0748:70 codes | Other chronic respiratory diseases originating in the perinatal period |
| P279 | MCC | 0748:70 codes | Unspecified chronic respiratory disease originating in the perinatal period |
| P280 | CC | 0748:70 codes | Primary atelectasis of newborn |
| P2810 | CC | 0748:70 codes | Unspecified atelectasis of newborn |
| P2811 | CC | 0748:70 codes | Resorption atelectasis without respiratory distress syndrome |
| P2819 | CC | 0748:70 codes | Other atelectasis of newborn |
| P282 | CC | 1024:10 codes | Cyanotic attacks of newborn |
| P283 | CC | 1025:8 codes | Primary sleep apnea of newborn |
| P284 | CC | 1026:9 codes | Other apnea of newborn |
| P285 | MCC | 0748:70 codes | Respiratory failure of newborn |
| P2881 | MCC | 1027:17 codes | Respiratory arrest of newborn |
| P2930 | MCC | 1028:11 codes | Pulmonary hypertension of newborn |
| P2938 | MCC | 1028:11 codes | Other persistent fetal circulation |
| P2981 | MCC | 1029:1 code | Cardiac arrest of newborn |
| P350 | CC | 1030:31 codes | Congenital rubella syndrome |
| P351 | MCC | 1030:31 codes | Congenital cytomegalovirus infection |
| P352 | MCC | 0562:193 codes | Congenital herpesviral [herpes simplex] infection |
| P353 | MCC | 0562:193 codes | Congenital viral hepatitis |
| P354 | MCC | 0562:193 codes | Congenital Zika virus disease |
| P358 | MCC | 0562:193 codes | Other congenital viral diseases |
| P359 | MCC | 0562:193 codes | Congenital viral disease, unspecified |
| P360 | MCC | 1031:48 codes | Sepsis of newborn due to streptococcus, group B |
| P3610 | MCC | 1031:48 codes | Sepsis of newborn due to unspecified streptococci |
| P3619 | MCC | 1031:48 codes | Sepsis of newborn due to other streptococci |
| P362 | MCC | 1031:48 codes | Sepsis of newborn due to Staphylococcus aureus |
| P3630 | MCC | 1031:48 codes | Sepsis of newborn due to unspecified staphylococci |
| P3639 | MCC | 1031:48 codes | Sepsis of newborn due to other staphylococci |
| P364 | MCC | 1031:48 codes | Sepsis of newborn due to Escherichia coli |
| P365 | MCC | 1031:48 codes | Sepsis of newborn due to anaerobes |
| P368 | MCC | 1031:48 codes | Other bacterial sepsis of newborn |
| P369 | MCC | 1031:48 codes | Bacterial sepsis of newborn, unspecified |
| P370 | MCC | 0562:193 codes | Congenital tuberculosis |
| P371 | MCC | 0562:193 codes | Congenital toxoplasmosis |
| P372 | MCC | 0562:193 codes | Neonatal (disseminated) listeriosis |
| P373 | MCC | 0562:193 codes | Congenital falciparum malaria |
| P374 | MCC | 0562:193 codes | Other congenital malaria |
| P378 | MCC | 0562:193 codes | Other specified congenital infectious and parasitic diseases |
| P379 | MCC | 0562:193 codes | Congenital infectious or parasitic disease, unspecified |
| P381 | CC | 1032:4 codes | Omphalitis with mild hemorrhage |
| P389 | CC | 1032:4 codes | Omphalitis without hemorrhage |
| P390 | CC | 1032:4 codes | Neonatal infective mastitis |
| P392 | CC | 1033:70 codes | Intra-amniotic infection affecting newborn, not elsewhere classified |
| P393 | CC | 1034:39 codes | Neonatal urinary tract infection |
| P394 | CC | 1033:70 codes | Neonatal skin infection |
| P398 | CC | 1033:70 codes | Other specified infections specific to the perinatal period |
| P399 | CC | 1033:70 codes | Infection specific to the perinatal period, unspecified |
| P520 | CC | 1021:48 codes | Intraventricular (nontraumatic) hemorrhage, grade 1, of newborn |
| P521 | CC | 1021:48 codes | Intraventricular (nontraumatic) hemorrhage, grade 2, of newborn |
| P5221 | MCC | 1021:48 codes | Intraventricular (nontraumatic) hemorrhage, grade 3, of newborn |
| P5222 | MCC | 1021:48 codes | Intraventricular (nontraumatic) hemorrhage, grade 4, of newborn |
| P523 | CC | 1021:48 codes | Unspecified intraventricular (nontraumatic) hemorrhage of newborn |
| P524 | MCC | 1020:39 codes | Intracerebral (nontraumatic) hemorrhage of newborn |
| P525 | MCC | 1022:49 codes | Subarachnoid (nontraumatic) hemorrhage of newborn |
| P526 | MCC | 1020:39 codes | Cerebellar (nontraumatic) and posterior fossa hemorrhage of newborn |
| P528 | MCC | 1020:39 codes | Other intracranial (nontraumatic) hemorrhages of newborn |
| P529 | MCC | 1020:39 codes | Intracranial (nontraumatic) hemorrhage of newborn, unspecified |
| P53 | CC | 1035:28 codes | Hemorrhagic disease of newborn |
| P541 | MCC | 1036:44 codes | Neonatal melena |
| P542 | MCC | 1036:44 codes | Neonatal rectal hemorrhage |
| P543 | MCC | 1036:44 codes | Other neonatal gastrointestinal hemorrhage |
| P544 | CC | 1036:44 codes | Neonatal adrenal hemorrhage |
| P560 | MCC | 1037:25 codes | Hydrops fetalis due to isoimmunization |
| P5690 | MCC | 1037:25 codes | Hydrops fetalis due to unspecified hemolytic disease |
| P5699 | MCC | 1037:25 codes | Hydrops fetalis due to other hemolytic disease |
| P570 | MCC | 1037:25 codes | Kernicterus due to isoimmunization |
| P578 | MCC | 1038:35 codes | Other specified kernicterus |
| P579 | MCC | 1038:35 codes | Kernicterus, unspecified |
| P591 | MCC | 1038:35 codes | Inspissated bile syndrome |
| P5920 | MCC | 1038:35 codes | Neonatal jaundice from unspecified hepatocellular damage |
| P5929 | MCC | 1038:35 codes | Neonatal jaundice from other hepatocellular damage |
| P60 | MCC | 1035:28 codes | Disseminated intravascular coagulation of newborn |
| P610 | MCC | 1035:28 codes | Transient neonatal thrombocytopenia |
| P612 | CC | 1039:84 codes | Anemia of prematurity |
| P613 | CC | 1039:84 codes | Congenital anemia from fetal blood loss |
| P614 | CC | 1039:84 codes | Other congenital anemias, not elsewhere classified |
| P615 | MCC | 1040:62 codes | Transient neonatal neutropenia |
| P616 | CC | 1035:28 codes | Other transient neonatal disorders of coagulation |
| P702 | CC | 1041:44 codes | Neonatal diabetes mellitus |
| P708 | CC | 1042:27 codes | Other transitory disorders of carbohydrate metabolism of newborn |
| P710 | CC | 1041:44 codes | Cow's milk hypocalcemia in newborn |
| P711 | CC | 1041:44 codes | Other neonatal hypocalcemia |
| P712 | CC | 1041:44 codes | Neonatal hypomagnesemia |
| P713 | CC | 1041:44 codes | Neonatal tetany without calcium or magnesium deficiency |
| P714 | CC | 1041:44 codes | Transitory neonatal hypoparathyroidism |
| P718 | CC | 1041:44 codes | Other transitory neonatal disorders of calcium and magnesium metabolism |
| P719 | CC | 1041:44 codes | Transitory neonatal disorder of calcium and magnesium metabolism, unspecified |
| P720 | CC | 1042:27 codes | Neonatal goiter, not elsewhere classified |
| P721 | CC | 1041:44 codes | Transitory neonatal hyperthyroidism |
| P722 | CC | 1042:27 codes | Other transitory neonatal disorders of thyroid function, not elsewhere classified |
| P728 | CC | 1042:27 codes | Other specified transitory neonatal endocrine disorders |
| P740 | MCC | 1041:44 codes | Late metabolic acidosis of newborn |
| P7441 | CC | 1042:27 codes | Alkalosis of newborn |
| P745 | CC | 1042:27 codes | Transitory tyrosinemia of newborn |
| P746 | CC | 1042:27 codes | Transitory hyperammonemia of newborn |
| P748 | CC | 1042:27 codes | Other transitory metabolic disturbances of newborn |
| P761 | CC | 1043:19 codes | Transitory ileus of newborn |
| P771 | MCC | 1044:36 codes | Stage 1 necrotizing enterocolitis in newborn |
| P772 | MCC | 1044:36 codes | Stage 2 necrotizing enterocolitis in newborn |
| P773 | MCC | 1044:36 codes | Stage 3 necrotizing enterocolitis in newborn |
| P779 | MCC | 1044:36 codes | Necrotizing enterocolitis in newborn, unspecified |
| P780 | MCC | 1044:36 codes | Perinatal intestinal perforation |
| P830 | CC | 1045:3 codes | Sclerema neonatorum |
| P832 | MCC | 1046:18 codes | Hydrops fetalis not due to hemolytic disease |
| P8330 | CC | 1047:9 codes | Unspecified edema specific to newborn |
| P8339 | CC | 1047:9 codes | Other edema specific to newborn |
| P90 | MCC | 1048:22 codes | Convulsions of newborn |
| P910 | MCC | 1049:10 codes | Neonatal cerebral ischemia |
| P911 | MCC | 1049:10 codes | Acquired periventricular cysts of newborn |
| P912 | MCC | 1022:49 codes | Neonatal cerebral leukomalacia |
| P913 | MCC | 1049:10 codes | Neonatal cerebral irritability |
| P914 | MCC | 1049:10 codes | Neonatal cerebral depression |
| P915 | MCC | 1049:10 codes | Neonatal coma |
| P9160 | CC | 1050:5 codes | Hypoxic ischemic encephalopathy [HIE], unspecified |
| P9161 | CC | 1050:5 codes | Mild hypoxic ischemic encephalopathy [HIE] |
| P9162 | CC | 1050:5 codes | Moderate hypoxic ischemic encephalopathy [HIE] |
| P9163 | MCC | 1050:5 codes | Severe hypoxic ischemic encephalopathy [HIE] |
| P9201 | MCC | 1051:2 codes | Bilious vomiting of newborn |
| P930 | CC | 1052:4 codes | Grey baby syndrome |
| P938 | CC | 1052:4 codes | Other reactions and intoxications due to drugs administered to newborn |
| P940 | CC | 1041:44 codes | Transient neonatal myasthenia gravis |
| P961 | CC | 1052:4 codes | Neonatal withdrawal symptoms from maternal use of drugs of addiction |
| P962 | CC | 1052:4 codes | Withdrawal symptoms from therapeutic use of drugs in newborn |
| Q000 | MCC | 1053:3 codes | Anencephaly |
| Q001 | MCC | 1053:3 codes | Craniorachischisis |
| Q002 | MCC | 1053:3 codes | Iniencephaly |
| Q010 | CC | 1054:14 codes | Frontal encephalocele |
| Q011 | CC | 1054:14 codes | Nasofrontal encephalocele |
| Q012 | CC | 1054:14 codes | Occipital encephalocele |
| Q018 | CC | 1054:14 codes | Encephalocele of other sites |
| Q019 | CC | 1054:14 codes | Encephalocele, unspecified |
| Q040 | MCC | 1054:14 codes | Congenital malformations of corpus callosum |
| Q041 | MCC | 1054:14 codes | Arhinencephaly |
| Q042 | MCC | 1054:14 codes | Holoprosencephaly |
| Q043 | MCC | 1054:14 codes | Other reduction deformities of brain |
| Q044 | CC | 1055:4 codes | Septo-optic dysplasia of brain |
| Q045 | CC | 1055:4 codes | Megalencephaly |
| Q046 | CC | 1055:4 codes | Congenital cerebral cysts |
| Q048 | CC | 1055:4 codes | Other specified congenital malformations of brain |
| Q050 | CC | 1056:39 codes | Cervical spina bifida with hydrocephalus |
| Q051 | CC | 1056:39 codes | Thoracic spina bifida with hydrocephalus |
| Q052 | CC | 1056:39 codes | Lumbar spina bifida with hydrocephalus |
| Q053 | CC | 1056:39 codes | Sacral spina bifida with hydrocephalus |
| Q054 | CC | 1056:39 codes | Unspecified spina bifida with hydrocephalus |
| Q0702 | CC | 1056:39 codes | Arnold-Chiari syndrome with hydrocephalus |
| Q0703 | CC | 1056:39 codes | Arnold-Chiari syndrome with spina bifida and hydrocephalus |
| Q200 | MCC | 1057:53 codes | Common arterial trunk |
| Q201 | MCC | 1057:53 codes | Double outlet right ventricle |
| Q202 | MCC | 1057:53 codes | Double outlet left ventricle |
| Q203 | MCC | 1057:53 codes | Discordant ventriculoarterial connection |
| Q204 | MCC | 1057:53 codes | Double inlet ventricle |
| Q205 | CC | 1057:53 codes | Discordant atrioventricular connection |
| Q210 | CC | 1057:53 codes | Ventricular septal defect |
| Q211 | CC | 1058:43 codes | Atrial septal defect |
| Q212 | CC | 1057:53 codes | Atrioventricular septal defect |
| Q213 | MCC | 1057:53 codes | Tetralogy of Fallot |
| Q220 | MCC | 1059:34 codes | Pulmonary valve atresia |
| Q221 | CC | 1059:34 codes | Congenital pulmonary valve stenosis |
| Q222 | CC | 1060:25 codes | Congenital pulmonary valve insufficiency |
| Q223 | CC | 1060:25 codes | Other congenital malformations of pulmonary valve |
| Q224 | MCC | 1061:40 codes | Congenital tricuspid stenosis |
| Q225 | MCC | 1061:40 codes | Ebstein's anomaly |
| Q226 | MCC | 1061:40 codes | Hypoplastic right heart syndrome |
| Q228 | MCC | 1061:40 codes | Other congenital malformations of tricuspid valve |
| Q229 | MCC | 1061:40 codes | Congenital malformation of tricuspid valve, unspecified |
| Q230 | CC | 1061:40 codes | Congenital stenosis of aortic valve |
| Q231 | CC | 1061:40 codes | Congenital insufficiency of aortic valve |
| Q232 | CC | 1061:40 codes | Congenital mitral stenosis |
| Q233 | CC | 1061:40 codes | Congenital mitral insufficiency |
| Q234 | MCC | 1061:40 codes | Hypoplastic left heart syndrome |
| Q240 | CC | 1062:26 codes | Dextrocardia |
| Q241 | CC | 1062:26 codes | Levocardia |
| Q242 | MCC | 1063:33 codes | Cor triatriatum |
| Q243 | CC | 1063:33 codes | Pulmonary infundibular stenosis |
| Q244 | MCC | 1063:33 codes | Congenital subaortic stenosis |
| Q245 | CC | 1064:6 codes | Malformation of coronary vessels |
| Q246 | MCC | 1065:31 codes | Congenital heart block |
| Q250 | CC | 1066:6 codes | Patent ductus arteriosus |
| Q251 | CC | 1067:20 codes | Coarctation of aorta |
| Q2521 | CC | 1068:29 codes | Interruption of aortic arch |
| Q2529 | CC | 1068:29 codes | Other atresia of aorta |
| Q253 | CC | 1068:29 codes | Supravalvular aortic stenosis |
| Q2540 | CC | 1069:32 codes | Congenital malformation of aorta unspecified |
| Q2541 | CC | 1069:32 codes | Absence and aplasia of aorta |
| Q2542 | CC | 1069:32 codes | Hypoplasia of aorta |
| Q2543 | CC | 1069:32 codes | Congenital aneurysm of aorta |
| Q2544 | CC | 1069:32 codes | Congenital dilation of aorta |
| Q2545 | CC | 1069:32 codes | Double aortic arch |
| Q2546 | CC | 1069:32 codes | Tortuous aortic arch |
| Q2547 | CC | 1069:32 codes | Right aortic arch |
| Q2548 | CC | 1069:32 codes | Anomalous origin of subclavian artery |
| Q2549 | CC | 1069:32 codes | Other congenital malformations of aorta |
| Q255 | MCC | 1070:11 codes | Atresia of pulmonary artery |
| Q256 | MCC | 1070:11 codes | Stenosis of pulmonary artery |
| Q2571 | MCC | 1070:11 codes | Coarctation of pulmonary artery |
| Q2572 | MCC | 1070:11 codes | Congenital pulmonary arteriovenous malformation |
| Q2579 | MCC | 1070:11 codes | Other congenital malformations of pulmonary artery |
| Q258 | CC | 1069:32 codes | Other congenital malformations of other great arteries |
| Q259 | CC | 1069:32 codes | Congenital malformation of great arteries, unspecified |
| Q260 | CC | 1071:9 codes | Congenital stenosis of vena cava |
| Q261 | CC | 1071:9 codes | Persistent left superior vena cava |
| Q262 | CC | 1072:7 codes | Total anomalous pulmonary venous connection |
| Q263 | CC | 1073:8 codes | Partial anomalous pulmonary venous connection |
| Q264 | CC | 1073:8 codes | Anomalous pulmonary venous connection, unspecified |
| Q268 | CC | 1071:9 codes | Other congenital malformations of great veins |
| Q269 | CC | 1074:7 codes | Congenital malformation of great vein, unspecified |
| Q2730 | CC | 1075:20 codes | Arteriovenous malformation, site unspecified |
| Q274 | CC | 1075:20 codes | Congenital phlebectasia |
| Q280 | CC | 1075:20 codes | Arteriovenous malformation of precerebral vessels |
| Q281 | CC | 1075:20 codes | Other malformations of precerebral vessels |
| Q282 | MCC | 1076:8 codes | Arteriovenous malformation of cerebral vessels |
| Q283 | MCC | 1076:8 codes | Other malformations of cerebral vessels |
| Q288 | CC | 1075:20 codes | Other specified congenital malformations of circulatory system |
| Q289 | CC | 1077:90 codes | Congenital malformation of circulatory system, unspecified |
| Q311 | CC | 1078:18 codes | Congenital subglottic stenosis |
| Q312 | CC | 1078:18 codes | Laryngeal hypoplasia |
| Q313 | CC | 1078:18 codes | Laryngocele |
| Q315 | CC | 1078:18 codes | Congenital laryngomalacia |
| Q318 | CC | 1078:18 codes | Other congenital malformations of larynx |
| Q319 | CC | 1078:18 codes | Congenital malformation of larynx, unspecified |
| Q320 | CC | 1078:18 codes | Congenital tracheomalacia |
| Q321 | CC | 1078:18 codes | Other congenital malformations of trachea |
| Q322 | CC | 1078:18 codes | Congenital bronchomalacia |
| Q323 | CC | 1078:18 codes | Congenital stenosis of bronchus |
| Q324 | CC | 1078:18 codes | Other congenital malformations of bronchus |
| Q330 | CC | 1079:13 codes | Congenital cystic lung |
| Q332 | MCC | 1079:13 codes | Sequestration of lung |
| Q333 | MCC | 1079:13 codes | Agenesis of lung |
| Q334 | CC | 1080:9 codes | Congenital bronchiectasis |
| Q336 | MCC | 1079:13 codes | Congenital hypoplasia and dysplasia of lung |
| Q390 | MCC | 1081:11 codes | Atresia of esophagus without fistula |
| Q391 | MCC | 1081:11 codes | Atresia of esophagus with tracheo-esophageal fistula |
| Q392 | MCC | 1081:11 codes | Congenital tracheo-esophageal fistula without atresia |
| Q393 | MCC | 1081:11 codes | Congenital stenosis and stricture of esophagus |
| Q394 | MCC | 1081:11 codes | Esophageal web |
| Q395 | CC | 1082:6 codes | Congenital dilatation of esophagus |
| Q396 | CC | 1082:6 codes | Congenital diverticulum of esophagus |
| Q398 | CC | 1082:6 codes | Other congenital malformations of esophagus |
| Q399 | CC | 1082:6 codes | Congenital malformation of esophagus, unspecified |
| Q410 | CC | 1083:7 codes | Congenital absence, atresia and stenosis of duodenum |
| Q411 | CC | 1083:7 codes | Congenital absence, atresia and stenosis of jejunum |
| Q412 | CC | 1083:7 codes | Congenital absence, atresia and stenosis of ileum |
| Q418 | CC | 1083:7 codes | Congenital absence, atresia and stenosis of other specified parts of small intestine |
| Q419 | CC | 1083:7 codes | Congenital absence, atresia and stenosis of small intestine, part unspecified |
| Q420 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of rectum with fistula |
| Q421 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of rectum without fistula |
| Q422 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of anus with fistula |
| Q423 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of anus without fistula |
| Q428 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of other parts of large intestine |
| Q429 | CC | 1084:8 codes | Congenital absence, atresia and stenosis of large intestine, part unspecified |
| Q431 | CC | 1085:4 codes | Hirschsprung's disease |
| Q432 | CC | 1085:4 codes | Other congenital functional disorders of colon |
| Q433 | CC | 1086:7 codes | Congenital malformations of intestinal fixation |
| Q434 | CC | 1087:21 codes | Duplication of intestine |
| Q435 | CC | 1087:21 codes | Ectopic anus |
| Q436 | CC | 1087:21 codes | Congenital fistula of rectum and anus |
| Q437 | CC | 1087:21 codes | Persistent cloaca |
| Q438 | CC | 1087:21 codes | Other specified congenital malformations of intestine |
| Q439 | CC | 1087:21 codes | Congenital malformation of intestine, unspecified |
| Q440 | CC | 1088:8 codes | Agenesis, aplasia and hypoplasia of gallbladder |
| Q441 | CC | 1088:8 codes | Other congenital malformations of gallbladder |
| Q442 | MCC | 1089:4 codes | Atresia of bile ducts |
| Q443 | MCC | 1089:4 codes | Congenital stenosis and stricture of bile ducts |
| Q444 | CC | 1088:8 codes | Choledochal cyst |
| Q445 | CC | 1088:8 codes | Other congenital malformations of bile ducts |
| Q446 | CC | 1090:6 codes | Cystic disease of liver |
| Q447 | CC | 1088:8 codes | Other congenital malformations of liver |
| Q450 | CC | 1091:6 codes | Agenesis, aplasia and hypoplasia of pancreas |
| Q451 | CC | 1091:6 codes | Annular pancreas |
| Q452 | CC | 1091:6 codes | Congenital pancreatic cyst |
| Q453 | CC | 1091:6 codes | Other congenital malformations of pancreas and pancreatic duct |
| Q600 | CC | 1092:8 codes | Renal agenesis, unilateral |
| Q601 | CC | 1092:8 codes | Renal agenesis, bilateral |
| Q602 | CC | 1092:8 codes | Renal agenesis, unspecified |
| Q603 | CC | 1092:8 codes | Renal hypoplasia, unilateral |
| Q604 | CC | 1092:8 codes | Renal hypoplasia, bilateral |
| Q605 | CC | 1092:8 codes | Renal hypoplasia, unspecified |
| Q606 | CC | 1092:8 codes | Potter's syndrome |
| Q6100 | CC | 1093:3 codes | Congenital renal cyst, unspecified |
| Q6101 | CC | 1094:2 codes | Congenital single renal cyst |
| Q6102 | CC | 1095:4 codes | Congenital multiple renal cysts |
| Q6111 | CC | 1096:5 codes | Cystic dilatation of collecting ducts |
| Q6119 | CC | 1096:5 codes | Other polycystic kidney, infantile type |
| Q612 | CC | 1096:5 codes | Polycystic kidney, adult type |
| Q613 | CC | 1096:5 codes | Polycystic kidney, unspecified |
| Q614 | CC | 1097:2 codes | Renal dysplasia |
| Q615 | CC | 1095:4 codes | Medullary cystic kidney |
| Q618 | CC | 1095:4 codes | Other cystic kidney diseases |
| Q619 | CC | 1093:3 codes | Cystic kidney disease, unspecified |
| Q620 | CC | 1098:7 codes | Congenital hydronephrosis |
| Q6210 | CC | 1098:7 codes | Congenital occlusion of ureter, unspecified |
| Q6211 | CC | 1098:7 codes | Congenital occlusion of ureteropelvic junction |
| Q6212 | CC | 1098:7 codes | Congenital occlusion of ureterovesical orifice |
| Q622 | CC | 1098:7 codes | Congenital megaureter |
| Q6231 | CC | 1098:7 codes | Congenital ureterocele, orthotopic |
| Q6232 | CC | 1098:7 codes | Cecoureterocele |
| Q6239 | CC | 1098:7 codes | Other obstructive defects of renal pelvis and ureter |
| Q6410 | CC | 1099:7 codes | Exstrophy of urinary bladder, unspecified |
| Q6411 | CC | 1099:7 codes | Supravesical fissure of urinary bladder |
| Q6412 | CC | 1099:7 codes | Cloacal exstrophy of urinary bladder |
| Q6419 | CC | 1099:7 codes | Other exstrophy of urinary bladder |
| Q642 | CC | 1100:8 codes | Congenital posterior urethral valves |
| Q6431 | CC | 1100:8 codes | Congenital bladder neck obstruction |
| Q6432 | CC | 1100:8 codes | Congenital stricture of urethra |
| Q6433 | CC | 1100:8 codes | Congenital stricture of urinary meatus |
| Q6439 | CC | 1100:8 codes | Other atresia and stenosis of urethra and bladder neck |
| Q675 | CC | 1101:7 codes | Congenital deformity of spine |
| Q678 | CC | 1102:5 codes | Other congenital deformities of chest |
| Q681 | CC | 1102:5 codes | Congenital deformity of finger(s) and hand |
| Q743 | CC | 1102:5 codes | Arthrogryposis multiplex congenita |
| Q763 | CC | 1101:7 codes | Congenital scoliosis due to congenital bony malformation |
| Q76425 | CC | 1101:7 codes | Congenital lordosis, thoracolumbar region |
| Q76426 | CC | 1101:7 codes | Congenital lordosis, lumbar region |
| Q76427 | CC | 1101:7 codes | Congenital lordosis, lumbosacral region |
| Q76428 | CC | 1101:7 codes | Congenital lordosis, sacral and sacrococcygeal region |
| Q76429 | CC | 1101:7 codes | Congenital lordosis, unspecified region |
| Q766 | CC | 1103:6 codes | Other congenital malformations of ribs |
| Q767 | CC | 1103:6 codes | Congenital malformation of sternum |
| Q768 | CC | 1103:6 codes | Other congenital malformations of bony thorax |
| Q769 | CC | 1103:6 codes | Congenital malformation of bony thorax, unspecified |
| Q772 | CC | 1103:6 codes | Short rib syndrome |
| Q780 | CC | 1104:10 codes | Osteogenesis imperfecta |
| Q782 | CC | 1104:10 codes | Osteopetrosis |
| Q790 | MCC | 1105:3 codes | Congenital diaphragmatic hernia |
| Q791 | MCC | 1105:3 codes | Other congenital malformations of diaphragm |
| Q792 | MCC | 1106:5 codes | Exomphalos |
| Q793 | MCC | 1106:5 codes | Gastroschisis |
| Q794 | MCC | 1106:5 codes | Prune belly syndrome |
| Q7951 | MCC | 1106:5 codes | Congenital hernia of bladder |
| Q7959 | MCC | 1106:5 codes | Other congenital malformations of abdominal wall |
| Q796 | CC | 1107:1 code | Ehlers-Danlos syndrome |
| Q851 | CC | 1108:5 codes | Tuberous sclerosis |
| Q858 | CC | 1109:3 codes | Other phakomatoses, not elsewhere classified |
| Q859 | CC | 1109:3 codes | Phakomatosis, unspecified |
| Q871 | CC | 1110:20 codes | Congenital malformation syndromes predominantly associated with short stature |