| Dx | CC/MCC | Exclusions | Description |
| A000 | CC | 0002:3 codes | Cholera due to Vibrio cholerae 01, biovar cholerae |
| A001 | CC | 0002:3 codes | Cholera due to Vibrio cholerae 01, biovar eltor |
| A009 | CC | 0002:3 codes | Cholera, unspecified |
| A0100 | CC | 0003:11 codes | Typhoid fever, unspecified |
| A0101 | CC | 0003:11 codes | Typhoid meningitis |
| A0102 | CC | 0003:11 codes | Typhoid fever with heart involvement |
| A0103 | CC | 0003:11 codes | Typhoid pneumonia |
| A0104 | CC | 0003:11 codes | Typhoid arthritis |
| A0105 | CC | 0003:11 codes | Typhoid osteomyelitis |
| A0109 | CC | 0003:11 codes | Typhoid fever with other complications |
| A011 | CC | 0003:11 codes | Paratyphoid fever A |
| A012 | CC | 0003:11 codes | Paratyphoid fever B |
| A013 | CC | 0003:11 codes | Paratyphoid fever C |
| A014 | CC | 0003:11 codes | Paratyphoid fever, unspecified |
| A020 | CC | 0004:74 codes | Salmonella enteritis |
| A021 | MCC | 0005:105 codes | Salmonella sepsis |
| A0221 | MCC | 0006:66 codes | Salmonella meningitis |
| A0222 | MCC | 0007:114 codes | Salmonella pneumonia |
| A0223 | CC | 0008:1,010 codes | Salmonella arthritis |
| A0224 | CC | 0009:201 codes | Salmonella osteomyelitis |
| A0225 | CC | 0010:2 codes | Salmonella pyelonephritis |
| A0229 | CC | 0010:2 codes | Salmonella with other localized infection |
| A028 | CC | 0011:1 code | Other specified salmonella infections |
| A029 | CC | 0012:1 code | Salmonella infection, unspecified |
| A030 | CC | 0013:209 codes | Shigellosis due to Shigella dysenteriae |
| A040 | CC | 0014:76 codes | Enteropathogenic Escherichia coli infection |
| A041 | CC | 0014:76 codes | Enterotoxigenic Escherichia coli infection |
| A042 | CC | 0014:76 codes | Enteroinvasive Escherichia coli infection |
| A043 | CC | 0014:76 codes | Enterohemorrhagic Escherichia coli infection |
| A044 | CC | 0014:76 codes | Other intestinal Escherichia coli infections |
| A045 | CC | 0015:225 codes | Campylobacter enteritis |
| A046 | CC | 0015:225 codes | Enteritis due to Yersinia enterocolitica |
| A0471 | CC | 0015:225 codes | Enterocolitis due to Clostridium difficile, recurrent |
| A0472 | CC | 0015:225 codes | Enterocolitis due to Clostridium difficile, not specified as recurrent |
| A048 | CC | 0015:225 codes | Other specified bacterial intestinal infections |
| A049 | CC | 0016:99 codes | Bacterial intestinal infection, unspecified |
| A050 | CC | 0017:81 codes | Foodborne staphylococcal intoxication |
| A051 | CC | 0018:7 codes | Botulism food poisoning |
| A052 | CC | 0019:79 codes | Foodborne Clostridium perfringens [Clostridium welchii] intoxication |
| A053 | CC | 0017:81 codes | Foodborne Vibrio parahaemolyticus intoxication |
| A054 | CC | 0017:81 codes | Foodborne Bacillus cereus intoxication |
| A055 | CC | 0017:81 codes | Foodborne Vibrio vulnificus intoxication |
| A058 | CC | 0017:81 codes | Other specified bacterial foodborne intoxications |
| A060 | CC | 0020:3 codes | Acute amebic dysentery |
| A061 | CC | 0020:3 codes | Chronic intestinal amebiasis |
| A062 | CC | 0021:182 codes | Amebic nondysenteric colitis |
| A063 | CC | 0022:10 codes | Ameboma of intestine |
| A064 | MCC | 0023:2 codes | Amebic liver abscess |
| A065 | MCC | 0024:4 codes | Amebic lung abscess |
| A066 | MCC | 0025:2 codes | Amebic brain abscess |
| A0681 | CC | 0022:10 codes | Amebic cystitis |
| A0682 | CC | 0022:10 codes | Other amebic genitourinary infections |
| A0689 | CC | 0022:10 codes | Other amebic infections |
| A071 | CC | 0026:67 codes | Giardiasis [lambliasis] |
| A072 | CC | 0026:67 codes | Cryptosporidiosis |
| A073 | CC | 0026:67 codes | Isosporiasis |
| A074 | CC | 0027:73 codes | Cyclosporiasis |
| A078 | CC | 0026:67 codes | Other specified protozoal intestinal diseases |
| A079 | CC | 0026:67 codes | Protozoal intestinal disease, unspecified |
| A080 | CC | 0028:90 codes | Rotaviral enteritis |
| A0811 | CC | 0028:90 codes | Acute gastroenteropathy due to Norwalk agent |
| A0819 | CC | 0028:90 codes | Acute gastroenteropathy due to other small round viruses |
| A082 | CC | 0028:90 codes | Adenoviral enteritis |
| A0831 | CC | 0028:90 codes | Calicivirus enteritis |
| A0832 | CC | 0028:90 codes | Astrovirus enteritis |
| A0839 | CC | 0028:90 codes | Other viral enteritis |
| A09 | CC | 0017:81 codes | Infectious gastroenteritis and colitis, unspecified |
| A150 | CC | 0029:128 codes | Tuberculosis of lung |
| A154 | CC | 0029:128 codes | Tuberculosis of intrathoracic lymph nodes |
| A155 | CC | 0029:128 codes | Tuberculosis of larynx, trachea and bronchus |
| A156 | CC | 0029:128 codes | Tuberculous pleurisy |
| A157 | CC | 0030:50 codes | Primary respiratory tuberculosis |
| A158 | CC | 0031:21 codes | Other respiratory tuberculosis |
| A159 | CC | 0031:21 codes | Respiratory tuberculosis unspecified |
| A170 | MCC | 0032:67 codes | Tuberculous meningitis |
| A171 | MCC | 0032:67 codes | Meningeal tuberculoma |
| A1781 | MCC | 0033:24 codes | Tuberculoma of brain and spinal cord |
| A1782 | MCC | 0033:24 codes | Tuberculous meningoencephalitis |
| A1783 | MCC | 3209:1 code | Tuberculous neuritis |
| A1789 | MCC | 0034:22 codes | Other tuberculosis of nervous system |
| A179 | CC | 0035:20 codes | Tuberculosis of nervous system, unspecified |
| A1801 | CC | 0036:1 code | Tuberculosis of spine |
| A1802 | CC | 0037:1 code | Tuberculous arthritis of other joints |
| A1803 | CC | 0038:2 codes | Tuberculosis of other bones |
| A1809 | CC | 0039:3 codes | Other musculoskeletal tuberculosis |
| A1810 | CC | 0040:22 codes | Tuberculosis of genitourinary system, unspecified |
| A1811 | CC | 0041:25 codes | Tuberculosis of kidney and ureter |
| A1812 | CC | 0041:25 codes | Tuberculosis of bladder |
| A1813 | CC | 0041:25 codes | Tuberculosis of other urinary organs |
| A1814 | CC | 0042:24 codes | Tuberculosis of prostate |
| A1815 | CC | 0042:24 codes | Tuberculosis of other male genital organs |
| A1816 | CC | 0043:25 codes | Tuberculosis of cervix |
| A1817 | CC | 0043:25 codes | Tuberculous female pelvic inflammatory disease |
| A1818 | CC | 0043:25 codes | Tuberculosis of other female genital organs |
| A182 | CC | 0044:21 codes | Tuberculous peripheral lymphadenopathy |
| A1831 | MCC | 0045:24 codes | Tuberculous peritonitis |
| A1832 | CC | 0045:24 codes | Tuberculous enteritis |
| A1839 | CC | 0045:24 codes | Retroperitoneal tuberculosis |
| A184 | CC | 0030:50 codes | Tuberculosis of skin and subcutaneous tissue |
| A1850 | CC | 0046:26 codes | Tuberculosis of eye, unspecified |
| A1851 | CC | 0046:26 codes | Tuberculous episcleritis |
| A1852 | CC | 0046:26 codes | Tuberculous keratitis |
| A1853 | CC | 0046:26 codes | Tuberculous chorioretinitis |
| A1854 | CC | 0046:26 codes | Tuberculous iridocyclitis |
| A1859 | CC | 0046:26 codes | Other tuberculosis of eye |
| A186 | CC | 0047:21 codes | Tuberculosis of (inner) (middle) ear |
| A187 | CC | 0048:21 codes | Tuberculosis of adrenal glands |
| A1881 | CC | 0049:21 codes | Tuberculosis of thyroid gland |
| A1882 | CC | 0035:20 codes | Tuberculosis of other endocrine glands |
| A1883 | CC | 0045:24 codes | Tuberculosis of digestive tract organs, not elsewhere classified |
| A1884 | CC | 0035:20 codes | Tuberculosis of heart |
| A1885 | CC | 0050:21 codes | Tuberculosis of spleen |
| A1889 | CC | 0035:20 codes | Tuberculosis of other sites |
| A190 | MCC | 0051:25 codes | Acute miliary tuberculosis of a single specified site |
| A191 | MCC | 0051:25 codes | Acute miliary tuberculosis of multiple sites |
| A192 | MCC | 0051:25 codes | Acute miliary tuberculosis, unspecified |
| A198 | MCC | 0051:25 codes | Other miliary tuberculosis |
| A199 | MCC | 0051:25 codes | Miliary tuberculosis, unspecified |
| A200 | MCC | 0052:7 codes | Bubonic plague |
| A201 | MCC | 0052:7 codes | Cellulocutaneous plague |
| A202 | MCC | 0053:2 codes | Pneumonic plague |
| A203 | MCC | 0054:2 codes | Plague meningitis |
| A207 | MCC | 0055:49 codes | Septicemic plague |
| A208 | MCC | 0054:2 codes | Other forms of plague |
| A209 | MCC | 0056:1 code | Plague, unspecified |
| A210 | CC | 0057:1 code | Ulceroglandular tularemia |
| A211 | CC | 0058:2 codes | Oculoglandular tularemia |
| A212 | CC | 0059:79 codes | Pulmonary tularemia |
| A213 | CC | 0060:1 code | Gastrointestinal tularemia |
| A217 | CC | 0061:7 codes | Generalized tularemia |
| A218 | CC | 0061:7 codes | Other forms of tularemia |
| A219 | CC | 0061:7 codes | Tularemia, unspecified |
| A220 | CC | 0062:1 code | Cutaneous anthrax |
| A221 | MCC | 0063:123 codes | Pulmonary anthrax |
| A222 | CC | 0064:1 code | Gastrointestinal anthrax |
| A227 | MCC | 0005:105 codes | Anthrax sepsis |
| A228 | CC | 0065:1 code | Other forms of anthrax |
| A229 | CC | 0066:6 codes | Anthrax, unspecified |
| A238 | CC | 0067:6 codes | Other brucellosis |
| A239 | CC | 0067:6 codes | Brucellosis, unspecified |
| A240 | CC | 0068:1 code | Glanders |
| A241 | CC | 0069:4 codes | Acute and fulminating melioidosis |
| A242 | CC | 0069:4 codes | Subacute and chronic melioidosis |
| A243 | CC | 0069:4 codes | Other melioidosis |
| A249 | CC | 0069:4 codes | Melioidosis, unspecified |
| A250 | CC | 0070:3 codes | Spirillosis |
| A251 | CC | 0070:3 codes | Streptobacillosis |
| A259 | CC | 0070:3 codes | Rat-bite fever, unspecified |
| A267 | MCC | 0071:91 codes | Erysipelothrix sepsis |
| A270 | CC | 0072:4 codes | Leptospirosis icterohemorrhagica |
| A2781 | MCC | 0073:70 codes | Aseptic meningitis in leptospirosis |
| A2789 | CC | 0072:4 codes | Other forms of leptospirosis |
| A279 | CC | 0072:4 codes | Leptospirosis, unspecified |
| A280 | CC | 0074:14 codes | Pasteurellosis |
| A281 | CC | 0075:2 codes | Cat-scratch disease |
| A282 | CC | 0074:14 codes | Extraintestinal yersiniosis |
| A288 | CC | 0074:14 codes | Other specified zoonotic bacterial diseases, not elsewhere classified |
| A289 | CC | 0074:14 codes | Zoonotic bacterial disease, unspecified |
| A300 | CC | 0076:1 code | Indeterminate leprosy |
| A301 | CC | 0077:1 code | Tuberculoid leprosy |
| A302 | CC | 0078:3 codes | Borderline tuberculoid leprosy |
| A303 | CC | 0078:3 codes | Borderline leprosy |
| A304 | CC | 0078:3 codes | Borderline lepromatous leprosy |
| A305 | CC | 0079:1 code | Lepromatous leprosy |
| A308 | CC | 0080:1 code | Other forms of leprosy |
| A309 | CC | 0081:1 code | Leprosy, unspecified |
| A310 | CC | 0082:123 codes | Pulmonary mycobacterial infection |
| A311 | CC | 0083:5 codes | Cutaneous mycobacterial infection |
| A312 | CC | 0083:5 codes | Disseminated mycobacterium avium-intracellulare complex (DMAC) |
| A318 | CC | 0083:5 codes | Other mycobacterial infections |
| A319 | CC | 0083:5 codes | Mycobacterial infection, unspecified |
| A320 | CC | 0074:14 codes | Cutaneous listeriosis |
| A3211 | CC | 0074:14 codes | Listerial meningitis |
| A3212 | CC | 0074:14 codes | Listerial meningoencephalitis |
| A327 | MCC | 0071:91 codes | Listerial sepsis |
| A3281 | CC | 0074:14 codes | Oculoglandular listeriosis |
| A3282 | CC | 0074:14 codes | Listerial endocarditis |
| A3289 | CC | 0074:14 codes | Other forms of listeriosis |
| A329 | CC | 0074:14 codes | Listeriosis, unspecified |
| A33 | MCC | 0084:18 codes | Tetanus neonatorum |
| A34 | CC | 0085:271 codes | Obstetrical tetanus |
| A35 | MCC | 0086:5 codes | Other tetanus |
| A360 | CC | 0087:12 codes | Pharyngeal diphtheria |
| A361 | CC | 0087:12 codes | Nasopharyngeal diphtheria |
| A362 | CC | 0087:12 codes | Laryngeal diphtheria |
| A363 | CC | 0087:12 codes | Cutaneous diphtheria |
| A3681 | CC | 0088:29 codes | Diphtheritic cardiomyopathy |
| A3682 | CC | 0087:12 codes | Diphtheritic radiculomyelitis |
| A3683 | CC | 0087:12 codes | Diphtheritic polyneuritis |
| A3684 | CC | 0087:12 codes | Diphtheritic tubulo-interstitial nephropathy |
| A3685 | CC | 0087:12 codes | Diphtheritic cystitis |
| A3686 | CC | 0087:12 codes | Diphtheritic conjunctivitis |
| A3689 | CC | 0087:12 codes | Other diphtheritic complications |
| A369 | CC | 0087:12 codes | Diphtheria, unspecified |
| A3700 | CC | 0089:8 codes | Whooping cough due to Bordetella pertussis without pneumonia |
| A3701 | MCC | 0090:124 codes | Whooping cough due to Bordetella pertussis with pneumonia |
| A3710 | CC | 0089:8 codes | Whooping cough due to Bordetella parapertussis without pneumonia |
| A3711 | MCC | 0090:124 codes | Whooping cough due to Bordetella parapertussis with pneumonia |
| A3780 | CC | 0089:8 codes | Whooping cough due to other Bordetella species without pneumonia |
| A3781 | MCC | 0090:124 codes | Whooping cough due to other Bordetella species with pneumonia |
| A3790 | CC | 0089:8 codes | Whooping cough, unspecified species without pneumonia |
| A3791 | MCC | 0090:124 codes | Whooping cough, unspecified species with pneumonia |
| A380 | CC | 0091:8 codes | Scarlet fever with otitis media |
| A381 | CC | 0091:8 codes | Scarlet fever with myocarditis |
| A388 | CC | 0091:8 codes | Scarlet fever with other complications |
| A389 | CC | 0091:8 codes | Scarlet fever, uncomplicated |
| A390 | MCC | 0092:60 codes | Meningococcal meningitis |
| A391 | MCC | 0093:16 codes | Waterhouse-Friderichsen syndrome |
| A392 | MCC | 0094:48 codes | Acute meningococcemia |
| A393 | MCC | 0094:48 codes | Chronic meningococcemia |
| A394 | MCC | 0094:48 codes | Meningococcemia, unspecified |
| A3950 | MCC | 0095:16 codes | Meningococcal carditis, unspecified |
| A3951 | MCC | 0096:16 codes | Meningococcal endocarditis |
| A3952 | MCC | 0097:14 codes | Meningococcal myocarditis |
| A3953 | MCC | 0098:16 codes | Meningococcal pericarditis |
| A3981 | MCC | 0099:16 codes | Meningococcal encephalitis |
| A3982 | CC | 0100:16 codes | Meningococcal retrobulbar neuritis |
| A3983 | CC | 0101:17 codes | Meningococcal arthritis |
| A3984 | CC | 0101:17 codes | Postmeningococcal arthritis |
| A3989 | CC | 0102:15 codes | Other meningococcal infections |
| A399 | CC | 0102:15 codes | Meningococcal infection, unspecified |
| A400 | MCC | 0071:91 codes | Sepsis due to streptococcus, group A |
| A401 | MCC | 0071:91 codes | Sepsis due to streptococcus, group B |
| A403 | MCC | 3210:1 code | Sepsis due to Streptococcus pneumoniae |
| A408 | MCC | 0071:91 codes | Other streptococcal sepsis |
| A409 | MCC | 0071:91 codes | Streptococcal sepsis, unspecified |
| A4101 | MCC | 0071:91 codes | Sepsis due to Methicillin susceptible Staphylococcus aureus |
| A4102 | MCC | 0071:91 codes | Sepsis due to Methicillin resistant Staphylococcus aureus |
| A411 | MCC | 0071:91 codes | Sepsis due to other specified staphylococcus |
| A412 | MCC | 0071:91 codes | Sepsis due to unspecified staphylococcus |
| A413 | MCC | 0071:91 codes | Sepsis due to Hemophilus influenzae |
| A414 | MCC | 0071:91 codes | Sepsis due to anaerobes |
| A4150 | MCC | 0071:91 codes | Gram-negative sepsis, unspecified |
| A4151 | MCC | 0071:91 codes | Sepsis due to Escherichia coli [E. coli] |
| A4152 | MCC | 0071:91 codes | Sepsis due to Pseudomonas |
| A4153 | MCC | 0071:91 codes | Sepsis due to Serratia |
| A4159 | MCC | 0071:91 codes | Other Gram-negative sepsis |
| A4181 | MCC | 0071:91 codes | Sepsis due to Enterococcus |
| A4189 | MCC | 0071:91 codes | Other specified sepsis |
| A419 | MCC | 0071:91 codes | Sepsis, unspecified organism |
| A420 | CC | 0103:10 codes | Pulmonary actinomycosis |
| A421 | CC | 0104:8 codes | Abdominal actinomycosis |
| A422 | CC | 0105:8 codes | Cervicofacial actinomycosis |
| A427 | MCC | 0071:91 codes | Actinomycotic sepsis |
| A4281 | CC | 0106:14 codes | Actinomycotic meningitis |
| A4282 | CC | 0106:14 codes | Actinomycotic encephalitis |
| A4289 | CC | 0106:14 codes | Other forms of actinomycosis |
| A429 | CC | 0106:14 codes | Actinomycosis, unspecified |
| A430 | CC | 0103:10 codes | Pulmonary nocardiosis |
| A431 | CC | 0107:9 codes | Cutaneous nocardiosis |
| A438 | CC | 0106:14 codes | Other forms of nocardiosis |
| A439 | CC | 0106:14 codes | Nocardiosis, unspecified |
| A440 | CC | 0108:52 codes | Systemic bartonellosis |
| A441 | CC | 0108:52 codes | Cutaneous and mucocutaneous bartonellosis |
| A448 | CC | 0108:52 codes | Other forms of bartonellosis |
| A449 | CC | 0108:52 codes | Bartonellosis, unspecified |
| A480 | MCC | 0109:5 codes | Gas gangrene |
| A481 | MCC | 0110:120 codes | Legionnaires' disease |
| A483 | MCC | 0111:91 codes | Toxic shock syndrome |
| A4851 | CC | 0018:7 codes | Infant botulism |
| A4852 | CC | 0018:7 codes | Wound botulism |
| A5001 | CC | 0112:79 codes | Early congenital syphilitic oculopathy |
| A5002 | CC | 0112:79 codes | Early congenital syphilitic osteochondropathy |
| A5003 | CC | 0112:79 codes | Early congenital syphilitic pharyngitis |
| A5004 | CC | 0112:79 codes | Early congenital syphilitic pneumonia |
| A5005 | CC | 0112:79 codes | Early congenital syphilitic rhinitis |
| A5006 | CC | 0112:79 codes | Early cutaneous congenital syphilis |
| A5007 | CC | 0112:79 codes | Early mucocutaneous congenital syphilis |
| A5008 | CC | 0112:79 codes | Early visceral congenital syphilis |
| A5009 | CC | 0112:79 codes | Other early congenital syphilis, symptomatic |
| A502 | CC | 0113:153 codes | Early congenital syphilis, unspecified |
| A5030 | CC | 0112:79 codes | Late congenital syphilitic oculopathy, unspecified |
| A5031 | CC | 0112:79 codes | Late congenital syphilitic interstitial keratitis |
| A5032 | CC | 0112:79 codes | Late congenital syphilitic chorioretinitis |
| A5039 | CC | 0112:79 codes | Other late congenital syphilitic oculopathy |
| A5040 | CC | 0114:96 codes | Late congenital neurosyphilis, unspecified |
| A5041 | MCC | 0115:138 codes | Late congenital syphilitic meningitis |
| A5042 | MCC | 0114:96 codes | Late congenital syphilitic encephalitis |
| A5043 | CC | 0114:96 codes | Late congenital syphilitic polyneuropathy |
| A5044 | CC | 0112:79 codes | Late congenital syphilitic optic nerve atrophy |
| A5045 | CC | 0114:96 codes | Juvenile general paresis |
| A5049 | CC | 0114:96 codes | Other late congenital neurosyphilis |
| A5051 | CC | 0112:79 codes | Clutton's joints |
| A5052 | CC | 0112:79 codes | Hutchinson's teeth |
| A5053 | CC | 0112:79 codes | Hutchinson's triad |
| A5054 | CC | 0112:79 codes | Late congenital cardiovascular syphilis |
| A5055 | CC | 0112:79 codes | Late congenital syphilitic arthropathy |
| A5056 | CC | 0112:79 codes | Late congenital syphilitic osteochondropathy |
| A5057 | CC | 0112:79 codes | Syphilitic saddle nose |
| A5059 | CC | 0112:79 codes | Other late congenital syphilis, symptomatic |
| A5131 | CC | 0112:79 codes | Condyloma latum |
| A5132 | CC | 0116:149 codes | Syphilitic alopecia |
| A5139 | CC | 0112:79 codes | Other secondary syphilis of skin |
| A5141 | MCC | 0117:209 codes | Secondary syphilitic meningitis |
| A5142 | CC | 0113:153 codes | Secondary syphilitic female pelvic disease |
| A5143 | CC | 0112:79 codes | Secondary syphilitic oculopathy |
| A5144 | CC | 0113:153 codes | Secondary syphilitic nephritis |
| A5145 | CC | 0118:183 codes | Secondary syphilitic hepatitis |
| A5146 | CC | 0119:437 codes | Secondary syphilitic osteopathy |
| A5149 | CC | 3211:1 code | Other secondary syphilitic conditions |
| A5200 | CC | 0114:96 codes | Cardiovascular syphilis, unspecified |
| A5201 | CC | 0114:96 codes | Syphilitic aneurysm of aorta |
| A5202 | CC | 0114:96 codes | Syphilitic aortitis |
| A5203 | CC | 0114:96 codes | Syphilitic endocarditis |
| A5204 | CC | 0114:96 codes | Syphilitic cerebral arteritis |
| A5205 | CC | 0114:96 codes | Other cerebrovascular syphilis |
| A5206 | CC | 0114:96 codes | Other syphilitic heart involvement |
| A5209 | CC | 0114:96 codes | Other cardiovascular syphilis |
| A5210 | CC | 0114:96 codes | Symptomatic neurosyphilis, unspecified |
| A5211 | CC | 0114:96 codes | Tabes dorsalis |
| A5212 | CC | 0114:96 codes | Other cerebrospinal syphilis |
| A5213 | MCC | 0115:138 codes | Late syphilitic meningitis |
| A5214 | MCC | 0114:96 codes | Late syphilitic encephalitis |
| A5215 | CC | 0114:96 codes | Late syphilitic neuropathy |
| A5216 | CC | 0114:96 codes | Charcot's arthropathy (tabetic) |
| A5217 | CC | 0114:96 codes | General paresis |
| A5219 | CC | 0114:96 codes | Other symptomatic neurosyphilis |
| A522 | CC | 0114:96 codes | Asymptomatic neurosyphilis |
| A523 | CC | 0114:96 codes | Neurosyphilis, unspecified |
| A5271 | CC | 0120:175 codes | Late syphilitic oculopathy |
| A5272 | CC | 0116:149 codes | Syphilis of lung and bronchus |
| A5273 | CC | 0116:149 codes | Symptomatic late syphilis of other respiratory organs |
| A5274 | CC | 0116:149 codes | Syphilis of liver and other viscera |
| A5275 | CC | 0116:149 codes | Syphilis of kidney and ureter |
| A5276 | CC | 0116:149 codes | Other genitourinary symptomatic late syphilis |
| A5277 | CC | 0116:149 codes | Syphilis of bone and joint |
| A5278 | CC | 0116:149 codes | Syphilis of other musculoskeletal tissue |
| A5279 | CC | 0116:149 codes | Other symptomatic late syphilis |
| A5400 | CC | 0121:32 codes | Gonococcal infection of lower genitourinary tract, unspecified |
| A5401 | CC | 0121:32 codes | Gonococcal cystitis and urethritis, unspecified |
| A5402 | CC | 0121:32 codes | Gonococcal vulvovaginitis, unspecified |
| A5403 | CC | 0121:32 codes | Gonococcal cervicitis, unspecified |
| A5409 | CC | 0121:32 codes | Other gonococcal infection of lower genitourinary tract |
| A541 | CC | 0121:32 codes | Gonococcal infection of lower genitourinary tract with periurethral and accessory gland abscess |
| A5421 | CC | 0121:32 codes | Gonococcal infection of kidney and ureter |
| A5422 | CC | 0121:32 codes | Gonococcal prostatitis |
| A5423 | CC | 0121:32 codes | Gonococcal infection of other male genital organs |
| A5424 | CC | 0121:32 codes | Gonococcal female pelvic inflammatory disease |
| A5429 | CC | 0121:32 codes | Other gonococcal genitourinary infections |
| A5430 | CC | 0116:149 codes | Gonococcal infection of eye, unspecified |
| A5431 | CC | 0116:149 codes | Gonococcal conjunctivitis |
| A5432 | CC | 0116:149 codes | Gonococcal iridocyclitis |
| A5433 | CC | 0116:149 codes | Gonococcal keratitis |
| A5439 | CC | 0116:149 codes | Other gonococcal eye infection |
| A5440 | CC | 0122:1,146 codes | Gonococcal infection of musculoskeletal system, unspecified |
| A5441 | CC | 0122:1,146 codes | Gonococcal spondylopathy |
| A5442 | CC | 0122:1,146 codes | Gonococcal arthritis |
| A5443 | CC | 0122:1,146 codes | Gonococcal osteomyelitis |
| A5449 | CC | 0122:1,146 codes | Gonococcal infection of other musculoskeletal tissue |
| A5481 | MCC | 0117:209 codes | Gonococcal meningitis |
| A5482 | CC | 0123:151 codes | Gonococcal brain abscess |
| A5483 | CC | 0124:260 codes | Gonococcal heart infection |
| A5484 | CC | 0123:151 codes | Gonococcal pneumonia |
| A5485 | CC | 0125:183 codes | Gonococcal peritonitis |
| A5486 | MCC | 0071:91 codes | Gonococcal sepsis |
| A5489 | CC | 0123:151 codes | Other gonococcal infections |
| A549 | CC | 0123:151 codes | Gonococcal infection, unspecified |
| A680 | CC | 0108:52 codes | Louse-borne relapsing fever |
| A681 | CC | 0108:52 codes | Tick-borne relapsing fever |
| A689 | CC | 0108:52 codes | Relapsing fever, unspecified |
| A691 | CC | 0126:1 code | Other Vincent's infections |
| A6920 | CC | 0108:52 codes | Lyme disease, unspecified |
| A6921 | CC | 0108:52 codes | Meningitis due to Lyme disease |
| A6922 | CC | 0108:52 codes | Other neurologic disorders in Lyme disease |
| A6923 | CC | 0108:52 codes | Arthritis due to Lyme disease |
| A6929 | CC | 0108:52 codes | Other conditions associated with Lyme disease |
| A70 | CC | 0127:1 code | Chlamydia psittaci infections |
| A750 | CC | 0108:52 codes | Epidemic louse-borne typhus fever due to Rickettsia prowazekii |
| A751 | CC | 0108:52 codes | Recrudescent typhus [Brill's disease] |
| A752 | CC | 0108:52 codes | Typhus fever due to Rickettsia typhi |
| A753 | CC | 0108:52 codes | Typhus fever due to Rickettsia tsutsugamushi |
| A759 | CC | 0128:212 codes | Typhus fever, unspecified |
| A770 | CC | 0108:52 codes | Spotted fever due to Rickettsia rickettsii |
| A771 | CC | 0108:52 codes | Spotted fever due to Rickettsia conorii |
| A772 | CC | 0108:52 codes | Spotted fever due to Rickettsia siberica |
| A773 | CC | 0108:52 codes | Spotted fever due to Rickettsia australis |
| A7740 | CC | 0108:52 codes | Ehrlichiosis, unspecified |
| A7741 | CC | 0108:52 codes | Ehrlichiosis chafeensis [E. chafeensis] |
| A7749 | CC | 0108:52 codes | Other ehrlichiosis |
| A778 | CC | 0108:52 codes | Other spotted fevers |
| A779 | CC | 0108:52 codes | Spotted fever, unspecified |
| A78 | CC | 0108:52 codes | Q fever |
| A790 | CC | 0108:52 codes | Trench fever |
| A791 | CC | 0129:15 codes | Rickettsialpox due to Rickettsia akari |
| A7981 | CC | 0129:15 codes | Rickettsiosis due to Ehrlichia sennetsu |
| A7989 | CC | 0129:15 codes | Other specified rickettsioses |
| A799 | CC | 0129:15 codes | Rickettsiosis, unspecified |
| A800 | MCC | 0130:5 codes | Acute paralytic poliomyelitis, vaccine-associated |
| A801 | MCC | 0130:5 codes | Acute paralytic poliomyelitis, wild virus, imported |
| A802 | MCC | 0130:5 codes | Acute paralytic poliomyelitis, wild virus, indigenous |
| A8030 | MCC | 0130:5 codes | Acute paralytic poliomyelitis, unspecified |
| A8039 | MCC | 0130:5 codes | Other acute paralytic poliomyelitis |
| A8100 | CC | 0131:163 codes | Creutzfeldt-Jakob disease, unspecified |
| A8101 | CC | 0131:163 codes | Variant Creutzfeldt-Jakob disease |
| A8109 | CC | 0131:163 codes | Other Creutzfeldt-Jakob disease |
| A811 | CC | 0132:5 codes | Subacute sclerosing panencephalitis |
| A812 | CC | 0133:178 codes | Progressive multifocal leukoencephalopathy |
| A8181 | CC | 0134:11 codes | Kuru |
| A8182 | CC | 0135:16 codes | Gerstmann-Straussler-Scheinker syndrome |
| A8183 | CC | 0135:16 codes | Fatal familial insomnia |
| A8189 | CC | 0135:16 codes | Other atypical virus infections of central nervous system |