DRAFT
ICD-10-CM/PCS MS-DRG v43.0 Definitions Manual |
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| Part 1: List of CC and Major CC Codes |
| Page 5 of 47 |
| A000 A8182 C227 C8266 D57213 E8722 G115 H47511 I63441 I83224 K51919 L97106 M02819 M84321K M84758P M9050 O2313 O8621 Q391 S02630A S1201XK S22010B S32010B S3282XK S42135P S42416B S49139K S52209R S52321P S52514B S56229A S62201B S62605K S72019C S72125P S72355B S72461N S82014A S82136M S82261R S82491Q S85102A S92121P S95011A T3282 T82868A Z48290 |
| Dx | CC/MCC | Exclusions | Description |
|---|---|---|---|
| D57213 | MCC | 0497:49 codes | Sickle-cell/Hb-C disease with cerebral vascular involvement |
| D57214 | MCC | 0497:49 codes | Sickle-cell/Hb-C disease with dactylitis |
| D57218 | MCC | 0497:49 codes | Sickle-cell/Hb-C disease with crisis with other specified complication |
| D57219 | MCC | 0496:125 codes | Sickle-cell/Hb-C disease with crisis, unspecified |
| D57411 | MCC | 0496:125 codes | Sickle-cell thalassemia, unspecified, with acute chest syndrome |
| D57412 | MCC | 0496:125 codes | Sickle-cell thalassemia, unspecified, with splenic sequestration |
| D57413 | MCC | 0498:47 codes | Sickle-cell thalassemia, unspecified, with cerebral vascular involvement |
| D57414 | MCC | 0498:47 codes | Sickle-cell thalassemia, unspecified, with dactylitis |
| D57418 | MCC | 0498:47 codes | Sickle-cell thalassemia, unspecified, with crisis with other specified complication |
| D57419 | MCC | 0496:125 codes | Sickle-cell thalassemia, unspecified, with crisis |
| D57431 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with acute chest syndrome |
| D57432 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with splenic sequestration |
| D57433 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with cerebral vascular involvement |
| D57434 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with dactylitis |
| D57438 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with crisis with other specified complication |
| D57439 | MCC | 0499:51 codes | Sickle-cell thalassemia beta zero with crisis, unspecified |
| D57451 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with acute chest syndrome |
| D57452 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with splenic sequestration |
| D57453 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with cerebral vascular involvement |
| D57454 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with dactylitis |
| D57458 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with crisis with other specified complication |
| D57459 | MCC | 0499:51 codes | Sickle-cell thalassemia beta plus with crisis, unspecified |
| D57811 | MCC | 0496:125 codes | Other sickle-cell disorders with acute chest syndrome |
| D57812 | MCC | 0496:125 codes | Other sickle-cell disorders with splenic sequestration |
| D57813 | MCC | 0500:48 codes | Other sickle-cell disorders with cerebral vascular involvement |
| D57814 | MCC | 0500:48 codes | Other sickle-cell disorders with dactylitis |
| D57818 | MCC | 0500:48 codes | Other sickle-cell disorders with crisis with other specified complication |
| D57819 | MCC | 0496:125 codes | Other sickle-cell disorders with crisis, unspecified |
| D588 | CC | 0501:104 codes | Other specified hereditary hemolytic anemias |
| D589 | CC | 0501:104 codes | Hereditary hemolytic anemia, unspecified |
| D590 | CC | 0502:112 codes | Drug-induced autoimmune hemolytic anemia |
| D5910 | CC | 0503:16 codes | Autoimmune hemolytic anemia, unspecified |
| D5911 | CC | 0503:16 codes | Warm autoimmune hemolytic anemia |
| D5912 | CC | 0503:16 codes | Cold autoimmune hemolytic anemia |
| D5913 | CC | 0503:16 codes | Mixed type autoimmune hemolytic anemia |
| D5919 | CC | 0503:16 codes | Other autoimmune hemolytic anemia |
| D592 | CC | 0502:112 codes | Drug-induced nonautoimmune hemolytic anemia |
| D5930 | MCC | 0504:110 codes | Hemolytic-uremic syndrome, unspecified |
| D5931 | MCC | 0504:110 codes | Infection-associated hemolytic-uremic syndrome |
| D5932 | MCC | 0504:110 codes | Hereditary hemolytic-uremic syndrome |
| D5939 | MCC | 0504:110 codes | Other hemolytic-uremic syndrome |
| D594 | CC | 0504:110 codes | Other nonautoimmune hemolytic anemias |
| D599 | CC | 0504:110 codes | Acquired hemolytic anemia, unspecified |
| D600 | MCC | 0504:110 codes | Chronic acquired pure red cell aplasia |
| D601 | MCC | 0504:110 codes | Transient acquired pure red cell aplasia |
| D608 | MCC | 0504:110 codes | Other acquired pure red cell aplasias |
| D609 | MCC | 0504:110 codes | Acquired pure red cell aplasia, unspecified |
| D6101 | CC | 0505:98 codes | Constitutional (pure) red blood cell aplasia |
| D6102 | CC | 0506:101 codes | Shwachman-Diamond syndrome |
| D6103 | CC | 0507:102 codes | Fanconi anemia |
| D6109 | CC | 0507:102 codes | Other constitutional aplastic anemia |
| D611 | MCC | 0504:110 codes | Drug-induced aplastic anemia |
| D612 | MCC | 0504:110 codes | Aplastic anemia due to other external agents |
| D613 | MCC | 0504:110 codes | Idiopathic aplastic anemia |
| D61810 | MCC | 0508:41 codes | Antineoplastic chemotherapy induced pancytopenia |
| D61811 | MCC | 0508:41 codes | Other drug-induced pancytopenia |
| D61818 | CC | 0508:41 codes | Other pancytopenia |
| D6182 | CC | 0508:41 codes | Myelophthisis |
| D6189 | MCC | 0504:110 codes | Other specified aplastic anemias and other bone marrow failure syndromes |
| D619 | CC | 0504:110 codes | Aplastic anemia, unspecified |
| D62 | CC | 0509:111 codes | Acute posthemorrhagic anemia |
| D65 | MCC | 0510:50 codes | Disseminated intravascular coagulation [defibrination syndrome] |
| D66 | MCC | 0510:50 codes | Hereditary factor VIII deficiency |
| D67 | MCC | 0510:50 codes | Hereditary factor IX deficiency |
| D6800 | CC | 0511:49 codes | Von Willebrand disease, unspecified |
| D6801 | CC | 0511:49 codes | Von Willebrand disease, type 1 |
| D68020 | CC | 0511:49 codes | Von Willebrand disease, type 2A |
| D68021 | CC | 0511:49 codes | Von Willebrand disease, type 2B |
| D68022 | CC | 0511:49 codes | Von Willebrand disease, type 2M |
| D68023 | CC | 0511:49 codes | Von Willebrand disease, type 2N |
| D68029 | CC | 0511:49 codes | Von Willebrand disease, type 2, unspecified |
| D6803 | CC | 0511:49 codes | Von Willebrand disease, type 3 |
| D6804 | CC | 0511:49 codes | Acquired von Willebrand disease |
| D6809 | CC | 0511:49 codes | Other von Willebrand disease |
| D681 | CC | 0510:50 codes | Hereditary factor XI deficiency |
| D682 | CC | 0510:50 codes | Hereditary deficiency of other clotting factors |
| D68311 | CC | 0510:50 codes | Acquired hemophilia |
| D68312 | CC | 0512:52 codes | Antiphospholipid antibody with hemorrhagic disorder |
| D68318 | CC | 0510:50 codes | Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors |
| D6832 | CC | 0510:50 codes | Hemorrhagic disorder due to extrinsic circulating anticoagulants |
| D684 | CC | 0510:50 codes | Acquired coagulation factor deficiency |
| D6851 | CC | 0513:40 codes | Activated protein C resistance |
| D6852 | CC | 0513:40 codes | Prothrombin gene mutation |
| D6859 | CC | 0514:42 codes | Other primary thrombophilia |
| D6861 | CC | 0513:40 codes | Antiphospholipid syndrome |
| D6862 | CC | 0513:40 codes | Lupus anticoagulant syndrome |
| D6869 | CC | 0514:42 codes | Other thrombophilia |
| D688 | CC | 0510:50 codes | Other specified coagulation defects |
| D689 | CC | 0510:50 codes | Coagulation defect, unspecified |
| D690 | CC | 0510:50 codes | Allergic purpura |
| D693 | CC | 0515:52 codes | Immune thrombocytopenic purpura |
| D6941 | CC | 0515:52 codes | Evans syndrome |
| D6942 | CC | 0515:52 codes | Congenital and hereditary thrombocytopenia purpura |
| D740 | CC | 0516:24 codes | Congenital methemoglobinemia |
| D748 | CC | 0516:24 codes | Other methemoglobinemias |
| D749 | CC | 0516:24 codes | Methemoglobinemia, unspecified |
| D7581 | CC | 0487:133 codes | Myelofibrosis |
| D761 | CC | 0517:39 codes | Hemophagocytic lymphohistiocytosis |
| D762 | CC | 0518:39 codes | Hemophagocytic syndrome, infection-associated |
| D763 | CC | 0519:39 codes | Other histiocytosis syndromes |
| D7801 | CC | 0520:78 codes | Intraoperative hemorrhage and hematoma of the spleen complicating a procedure on the spleen |
| D7802 | CC | 0520:78 codes | Intraoperative hemorrhage and hematoma of the spleen complicating other procedure |
| D7811 | CC | 0521:76 codes | Accidental puncture and laceration of the spleen during a procedure on the spleen |
| D7812 | CC | 0521:76 codes | Accidental puncture and laceration of the spleen during other procedure |
| D7821 | CC | 0520:78 codes | Postprocedural hemorrhage of the spleen following a procedure on the spleen |
| D7822 | CC | 0520:78 codes | Postprocedural hemorrhage of the spleen following other procedure |
| D7831 | CC | 0520:78 codes | Postprocedural hematoma of the spleen following a procedure on the spleen |
| D7832 | CC | 0520:78 codes | Postprocedural hematoma of the spleen following other procedure |
| D7833 | CC | 0520:78 codes | Postprocedural seroma of the spleen following a procedure on the spleen |
| D7834 | CC | 0520:78 codes | Postprocedural seroma of the spleen following other procedure |
| D7881 | CC | 0522:18 codes | Other intraoperative complications of the spleen |
| D7889 | CC | 0522:18 codes | Other postprocedural complications of the spleen |
| D800 | CC | 0523:44 codes | Hereditary hypogammaglobulinemia |
| D801 | CC | 0524:46 codes | Nonfamilial hypogammaglobulinemia |
| D802 | CC | 0524:46 codes | Selective deficiency of immunoglobulin A [IgA] |
| D803 | CC | 0523:44 codes | Selective deficiency of immunoglobulin G [IgG] subclasses |
| D804 | CC | 0523:44 codes | Selective deficiency of immunoglobulin M [IgM] |
| D805 | CC | 0523:44 codes | Immunodeficiency with increased immunoglobulin M [IgM] |
| D806 | CC | 0523:44 codes | Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia |
| D807 | CC | 0523:44 codes | Transient hypogammaglobulinemia of infancy |
| D808 | CC | 0523:44 codes | Other immunodeficiencies with predominantly antibody defects |
| D809 | CC | 0523:44 codes | Immunodeficiency with predominantly antibody defects, unspecified |
| D810 | CC | 0523:44 codes | Severe combined immunodeficiency [SCID] with reticular dysgenesis |
| D811 | CC | 0523:44 codes | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
| D812 | CC | 0523:44 codes | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
| D8130 | CC | 0525:35 codes | Adenosine deaminase deficiency, unspecified |
| D8131 | CC | 0525:35 codes | Severe combined immunodeficiency due to adenosine deaminase deficiency |
| D8132 | CC | 0525:35 codes | Adenosine deaminase 2 deficiency |
| D8139 | CC | 0525:35 codes | Other adenosine deaminase deficiency |
| D814 | CC | 0523:44 codes | Nezelof's syndrome |
| D815 | CC | 0525:35 codes | Purine nucleoside phosphorylase [PNP] deficiency |
| D816 | CC | 0523:44 codes | Major histocompatibility complex class I deficiency |
| D817 | CC | 0523:44 codes | Major histocompatibility complex class II deficiency |
| D8182 | CC | 0523:44 codes | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
| D8189 | CC | 0523:44 codes | Other combined immunodeficiencies |
| D819 | CC | 0523:44 codes | Combined immunodeficiency, unspecified |
| D820 | CC | 0523:44 codes | Wiskott-Aldrich syndrome |
| D821 | CC | 0523:44 codes | Di George's syndrome |
| D830 | CC | 0523:44 codes | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function |
| D831 | CC | 0523:44 codes | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders |
| D832 | CC | 0523:44 codes | Common variable immunodeficiency with autoantibodies to B- or T-cells |
| D838 | CC | 0523:44 codes | Other common variable immunodeficiencies |
| D839 | CC | 0523:44 codes | Common variable immunodeficiency, unspecified |
| D8481 | CC | 0523:44 codes | Immunodeficiency due to conditions classified elsewhere |
| D84821 | CC | 0523:44 codes | Immunodeficiency due to drugs |
| D84822 | CC | 0523:44 codes | Immunodeficiency due to external causes |
| D8489 | CC | 0523:44 codes | Other immunodeficiencies |
| D849 | CC | 0523:44 codes | Immunodeficiency, unspecified |
| D89810 | CC | 0526:45 codes | Acute graft-versus-host disease |
| D89811 | CC | 0526:45 codes | Chronic graft-versus-host disease |
| D89812 | CC | 0526:45 codes | Acute on chronic graft-versus-host disease |
| D89813 | CC | 0526:45 codes | Graft-versus-host disease, unspecified |
| D89833 | CC | No Excl | Cytokine release syndrome, grade 3 |
| D89834 | CC | No Excl | Cytokine release syndrome, grade 4 |
| D89835 | CC | No Excl | Cytokine release syndrome, grade 5 |
| E035 | MCC | 0527:718 codes | Myxedema coma |
| E0501 | MCC | 0528:59 codes | Thyrotoxicosis with diffuse goiter with thyrotoxic crisis or storm |
| E0511 | MCC | 0528:59 codes | Thyrotoxicosis with toxic single thyroid nodule with thyrotoxic crisis or storm |
| E0521 | MCC | 0528:59 codes | Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis or storm |
| E0531 | MCC | 0528:59 codes | Thyrotoxicosis from ectopic thyroid tissue with thyrotoxic crisis or storm |
| E0541 | MCC | 0528:59 codes | Thyrotoxicosis factitia with thyrotoxic crisis or storm |
| E0581 | MCC | 0528:59 codes | Other thyrotoxicosis with thyrotoxic crisis or storm |
| E0591 | MCC | 0528:59 codes | Thyrotoxicosis, unspecified with thyrotoxic crisis or storm |
| E060 | CC | 0529:7 codes | Acute thyroiditis |
| E0800 | MCC | 0530:352 codes | Diabetes mellitus due to underlying condition with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) |
| E0801 | MCC | 0530:352 codes | Diabetes mellitus due to underlying condition with hyperosmolarity with coma |
| E0810 | MCC | 0530:352 codes | Diabetes mellitus due to underlying condition with ketoacidosis without coma |
| E0811 | MCC | 0530:352 codes | Diabetes mellitus due to underlying condition with ketoacidosis with coma |
| E0852 | CC | 0531:45 codes | Diabetes mellitus due to underlying condition with diabetic peripheral angiopathy with gangrene |
| E08641 | MCC | 0530:352 codes | Diabetes mellitus due to underlying condition with hypoglycemia with coma |
| E0900 | MCC | 0530:352 codes | Drug or chemical induced diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) |
| E0901 | MCC | 0530:352 codes | Drug or chemical induced diabetes mellitus with hyperosmolarity with coma |
| E0910 | MCC | 0530:352 codes | Drug or chemical induced diabetes mellitus with ketoacidosis without coma |
| E0911 | MCC | 0530:352 codes | Drug or chemical induced diabetes mellitus with ketoacidosis with coma |
| E0952 | CC | 0532:46 codes | Drug or chemical induced diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E09641 | MCC | 0530:352 codes | Drug or chemical induced diabetes mellitus with hypoglycemia with coma |
| E1010 | MCC | 0533:355 codes | Type 1 diabetes mellitus with ketoacidosis without coma |
| E1011 | MCC | 0533:355 codes | Type 1 diabetes mellitus with ketoacidosis with coma |
| E1052 | CC | 0534:46 codes | Type 1 diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E10641 | MCC | 0533:355 codes | Type 1 diabetes mellitus with hypoglycemia with coma |
| E1100 | MCC | 0530:352 codes | Type 2 diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) |
| E1101 | MCC | 0530:352 codes | Type 2 diabetes mellitus with hyperosmolarity with coma |
| E1110 | MCC | 0530:352 codes | Type 2 diabetes mellitus with ketoacidosis without coma |
| E1111 | MCC | 0530:352 codes | Type 2 diabetes mellitus with ketoacidosis with coma |
| E1152 | CC | 0535:46 codes | Type 2 diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E11641 | MCC | 0530:352 codes | Type 2 diabetes mellitus with hypoglycemia with coma |
| E1300 | MCC | 0530:352 codes | Other specified diabetes mellitus with hyperosmolarity without nonketotic hyperglycemic-hyperosmolar coma (NKHHC) |
| E1301 | MCC | 0530:352 codes | Other specified diabetes mellitus with hyperosmolarity with coma |
| E1310 | MCC | 0530:352 codes | Other specified diabetes mellitus with ketoacidosis without coma |
| E1311 | MCC | 0530:352 codes | Other specified diabetes mellitus with ketoacidosis with coma |
| E1352 | CC | 0536:46 codes | Other specified diabetes mellitus with diabetic peripheral angiopathy with gangrene |
| E13641 | MCC | 0530:352 codes | Other specified diabetes mellitus with hypoglycemia with coma |
| E15 | CC | 0533:355 codes | Nondiabetic hypoglycemic coma |
| E221 | CC | 0537:4 codes | Hyperprolactinemia |
| E222 | CC | 0538:18 codes | Syndrome of inappropriate secretion of antidiuretic hormone |
| E228 | CC | 0537:4 codes | Other hyperfunction of pituitary gland |
| E229 | CC | 0537:4 codes | Hyperfunction of pituitary gland, unspecified |
| E230 | CC | 0539:21 codes | Hypopituitarism |
| E232 | CC | 0540:19 codes | Diabetes insipidus |
| E240 | CC | 0541:23 codes | Pituitary-dependent Cushing's disease |
| E242 | CC | 0541:23 codes | Drug-induced Cushing's syndrome |
| E243 | CC | 0541:23 codes | Ectopic ACTH syndrome |
| E244 | CC | 0541:23 codes | Alcohol-induced pseudo-Cushing's syndrome |
| E248 | CC | 0541:23 codes | Other Cushing's syndrome |
| E249 | CC | 0541:23 codes | Cushing's syndrome, unspecified |
| E270 | CC | 0542:22 codes | Other adrenocortical overactivity |
| E271 | CC | 0542:22 codes | Primary adrenocortical insufficiency |
| E272 | CC | 0542:22 codes | Addisonian crisis |
| E273 | CC | 0542:22 codes | Drug-induced adrenocortical insufficiency |
| E2740 | CC | 0542:22 codes | Unspecified adrenocortical insufficiency |
| E2749 | CC | 0542:22 codes | Other adrenocortical insufficiency |
| E275 | CC | 0542:22 codes | Adrenomedullary hyperfunction |
| E321 | CC | 0543:11 codes | Abscess of thymus |
| E3400 | CC | 0544:11 codes | Carcinoid syndrome, unspecified |
| E3401 | CC | 0544:11 codes | Carcinoid heart syndrome |
| E3409 | CC | 0544:11 codes | Other carcinoid syndrome |
| E3601 | CC | 0545:78 codes | Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating an endocrine system procedure |
| E3602 | CC | 0545:78 codes | Intraoperative hemorrhage and hematoma of an endocrine system organ or structure complicating other procedure |
| E3611 | CC | 0521:76 codes | Accidental puncture and laceration of an endocrine system organ or structure during an endocrine system procedure |
| E3612 | CC | 0521:76 codes | Accidental puncture and laceration of an endocrine system organ or structure during other procedure |
| E40 | MCC | 0546:9 codes | Kwashiorkor |
| E41 | MCC | 0546:9 codes | Nutritional marasmus |
| E42 | MCC | 0546:9 codes | Marasmic kwashiorkor |
| E43 | MCC | 0546:9 codes | Unspecified severe protein-calorie malnutrition |
| E440 | CC | 0546:9 codes | Moderate protein-calorie malnutrition |
| E441 | CC | 0546:9 codes | Mild protein-calorie malnutrition |
| E45 | CC | 0546:9 codes | Retarded development following protein-calorie malnutrition |
| E46 | CC | 0546:9 codes | Unspecified protein-calorie malnutrition |
| E5111 | CC | 0547:34 codes | Dry beriberi |
| E5112 | CC | 0547:34 codes | Wet beriberi |
| E512 | CC | 0547:34 codes | Wernicke's encephalopathy |
| E518 | CC | 0547:34 codes | Other manifestations of thiamine deficiency |
| E519 | CC | 0547:34 codes | Thiamine deficiency, unspecified |
| E530 | CC | 0547:34 codes | Riboflavin deficiency |
| E550 | CC | 0548:34 codes | Rickets, active |
| E640 | CC | 0546:9 codes | Sequelae of protein-calorie malnutrition |
| E662 | CC | 0549:13 codes | Morbid (severe) obesity with alveolar hypoventilation |
| E700 | CC | 0550:140 codes | Classical phenylketonuria |
| E701 | CC | 0550:140 codes | Other hyperphenylalaninemias |
| E7020 | CC | 0550:140 codes | Disorder of tyrosine metabolism, unspecified |
| E7021 | CC | 0550:140 codes | Tyrosinemia |
| E7029 | CC | 0550:140 codes | Other disorders of tyrosine metabolism |
| E7030 | CC | 0550:140 codes | Albinism, unspecified |
| E70310 | CC | 0550:140 codes | X-linked ocular albinism |
| E70311 | CC | 0550:140 codes | Autosomal recessive ocular albinism |
| E70318 | CC | 0550:140 codes | Other ocular albinism |
| E70319 | CC | 0550:140 codes | Ocular albinism, unspecified |
| E70320 | CC | 0550:140 codes | Tyrosinase negative oculocutaneous albinism |
| E70321 | CC | 0550:140 codes | Tyrosinase positive oculocutaneous albinism |
| E70328 | CC | 0550:140 codes | Other oculocutaneous albinism |
| E70329 | CC | 0550:140 codes | Oculocutaneous albinism, unspecified |
| E70330 | CC | 0550:140 codes | Chediak-Higashi syndrome |
| E70331 | CC | 0550:140 codes | Hermansky-Pudlak syndrome |
| E70338 | CC | 0550:140 codes | Other albinism with hematologic abnormality |
| E70339 | CC | 0550:140 codes | Albinism with hematologic abnormality, unspecified |
| E7039 | CC | 0550:140 codes | Other specified albinism |
| E7040 | CC | 0550:140 codes | Disorders of histidine metabolism, unspecified |
| E7041 | CC | 0550:140 codes | Histidinemia |
| E7049 | CC | 0550:140 codes | Other disorders of histidine metabolism |
| E705 | CC | 0550:140 codes | Disorders of tryptophan metabolism |
| E7081 | CC | 0551:8 codes | Aromatic L-amino acid decarboxylase deficiency |
| E7089 | CC | 0551:8 codes | Other disorders of aromatic amino-acid metabolism |
| E709 | CC | 0550:140 codes | Disorder of aromatic amino-acid metabolism, unspecified |
| E710 | CC | 0550:140 codes | Maple-syrup-urine disease |
| E71110 | CC | 0550:140 codes | Isovaleric acidemia |
| E71111 | CC | 0550:140 codes | 3-methylglutaconic aciduria |
| E71118 | CC | 0550:140 codes | Other branched-chain organic acidurias |
| E71120 | CC | 0550:140 codes | Methylmalonic acidemia |
| E71121 | CC | 0550:140 codes | Propionic acidemia |
| E71128 | CC | 0550:140 codes | Other disorders of propionate metabolism |
| E7119 | CC | 0550:140 codes | Other disorders of branched-chain amino-acid metabolism |
| E712 | CC | 0550:140 codes | Disorder of branched-chain amino-acid metabolism, unspecified |
| E71310 | CC | 0552:39 codes | Long chain/very long chain acyl CoA dehydrogenase deficiency |
| E71311 | CC | 0553:39 codes | Medium chain acyl CoA dehydrogenase deficiency |
| E71312 | CC | 0554:39 codes | Short chain acyl CoA dehydrogenase deficiency |
| E71313 | CC | 0555:39 codes | Glutaric aciduria type II |
| E71314 | CC | 0556:39 codes | Muscle carnitine palmitoyltransferase deficiency |
| E71318 | CC | 0557:39 codes | Other disorders of fatty-acid oxidation |
| E7132 | CC | 0558:39 codes | Disorders of ketone metabolism |
| E7139 | CC | 0559:41 codes | Other disorders of fatty-acid metabolism |
| E7150 | CC | 0560:36 codes | Peroxisomal disorder, unspecified |
| E71510 | CC | 0561:36 codes | Zellweger syndrome |
| E71511 | CC | 0562:36 codes | Neonatal adrenoleukodystrophy |
| E71518 | CC | 0563:36 codes | Other disorders of peroxisome biogenesis |
| E71520 | CC | 0564:36 codes | Childhood cerebral X-linked adrenoleukodystrophy |
| E71521 | CC | 0565:36 codes | Adolescent X-linked adrenoleukodystrophy |
| E71522 | CC | 0566:36 codes | Adrenomyeloneuropathy |
| E71528 | CC | 0567:36 codes | Other X-linked adrenoleukodystrophy |
| E71529 | CC | 0568:36 codes | X-linked adrenoleukodystrophy, unspecified type |
| E7153 | CC | 0569:36 codes | Other group 2 peroxisomal disorders |
| E71540 | CC | 0570:36 codes | Rhizomelic chondrodysplasia punctata |
| E71541 | CC | 0571:36 codes | Zellweger-like syndrome |
| E71542 | CC | 0572:36 codes | Other group 3 peroxisomal disorders |
| E71548 | CC | 0573:36 codes | Other peroxisomal disorders |
| E7200 | CC | 0550:140 codes | Disorders of amino-acid transport, unspecified |
| E7201 | CC | 0550:140 codes | Cystinuria |
| E7202 | CC | 0550:140 codes | Hartnup's disease |
| E7203 | CC | 0574:1 code | Lowe's syndrome |
| E7204 | CC | 0550:140 codes | Cystinosis |
| E7209 | CC | 0550:140 codes | Other disorders of amino-acid transport |
| E7210 | CC | 0550:140 codes | Disorders of sulfur-bearing amino-acid metabolism, unspecified |
| E7211 | CC | 0550:140 codes | Homocystinuria |
| E7212 | CC | 0550:140 codes | Methylenetetrahydrofolate reductase deficiency |
| E7219 | CC | 0550:140 codes | Other disorders of sulfur-bearing amino-acid metabolism |
| E7220 | CC | 0550:140 codes | Disorder of urea cycle metabolism, unspecified |
| E7221 | CC | 0550:140 codes | Argininemia |
| E7222 | CC | 0550:140 codes | Arginosuccinic aciduria |
| E7223 | CC | 0550:140 codes | Citrullinemia |
| E7229 | CC | 0550:140 codes | Other disorders of urea cycle metabolism |
| E723 | CC | 0550:140 codes | Disorders of lysine and hydroxylysine metabolism |
| E724 | CC | 0550:140 codes | Disorders of ornithine metabolism |
| E7250 | CC | 0550:140 codes | Disorder of glycine metabolism, unspecified |
| E7251 | CC | 0550:140 codes | Non-ketotic hyperglycinemia |
| E7252 | CC | 0550:140 codes | Trimethylaminuria |
| E72530 | CC | 0575:144 codes | Primary hyperoxaluria, type 1 |
| E72538 | CC | 0575:144 codes | Other specified primary hyperoxaluria |
| E72539 | CC | 0575:144 codes | Primary hyperoxaluria, unspecified |
| E7259 | CC | 0550:140 codes | Other disorders of glycine metabolism |
| E7281 | CC | 0550:140 codes | Disorders of gamma aminobutyric acid metabolism |
| E7289 | CC | 0550:140 codes | Other specified disorders of amino-acid metabolism |
| E729 | CC | 0550:140 codes | Disorder of amino-acid metabolism, unspecified |
| E7400 | CC | 0550:140 codes | Glycogen storage disease, unspecified |
| E7401 | CC | 0550:140 codes | von Gierke disease |
| E7402 | CC | 0550:140 codes | Pompe disease |
| E7403 | CC | 0550:140 codes | Cori disease |
| E7404 | CC | 0550:140 codes | McArdle disease |
| E7405 | CC | 0576:137 codes | Lysosome-associated membrane protein 2 [LAMP2] deficiency |
| E7409 | CC | 0550:140 codes | Other glycogen storage disease |
| E7420 | CC | 0550:140 codes | Disorders of galactose metabolism, unspecified |
| E7421 | CC | 0550:140 codes | Galactosemia |
| E7429 | CC | 0550:140 codes | Other disorders of galactose metabolism |
| E744 | CC | 0550:140 codes | Disorders of pyruvate metabolism and gluconeogenesis |
| E74810 | CC | 0577:55 codes | Glucose transporter protein type 1 deficiency |
| E74818 | CC | 0577:55 codes | Other disorders of glucose transport |
| E74819 | CC | 0577:55 codes | Disorders of glucose transport, unspecified |
| E74820 | CC | 0577:55 codes | SLC13A5 Citrate Transporter Disorder |
| E74829 | CC | 0577:55 codes | Other disorders of citrate metabolism |
| E7489 | CC | 0577:55 codes | Other specified disorders of carbohydrate metabolism |
| E7500 | CC | 0578:26 codes | GM2 gangliosidosis, unspecified |
| E7501 | CC | 0578:26 codes | Sandhoff disease |
| E7502 | CC | 0578:26 codes | Tay-Sachs disease |
| E7509 | CC | 0578:26 codes | Other GM2 gangliosidosis |
| E7510 | CC | 0578:26 codes | Unspecified gangliosidosis |
| E7511 | CC | 0578:26 codes | Mucolipidosis IV |
| E7519 | CC | 0578:26 codes | Other gangliosidosis |
| E7523 | CC | 0579:24 codes | Krabbe disease |
| E7525 | CC | 0579:24 codes | Metachromatic leukodystrophy |
| E7526 | CC | 0579:24 codes | Sulfatase deficiency |
| E7527 | CC | 0579:24 codes | Pelizaeus-Merzbacher disease |
| E7528 | CC | 0579:24 codes | Canavan disease |
| E7529 | CC | 0579:24 codes | Other sphingolipidosis |
| E754 | CC | 0578:26 codes | Neuronal ceroid lipofuscinosis |
| E7601 | CC | 0580:37 codes | Hurler's syndrome |
| E7602 | CC | 0580:37 codes | Hurler-Scheie syndrome |
| E7603 | CC | 0580:37 codes | Scheie's syndrome |
| E761 | CC | 0580:37 codes | Mucopolysaccharidosis, type II |
| E76210 | CC | 0580:37 codes | Morquio A mucopolysaccharidoses |
| E76211 | CC | 0580:37 codes | Morquio B mucopolysaccharidoses |
| E76219 | CC | 0580:37 codes | Morquio mucopolysaccharidoses, unspecified |
| E7622 | CC | 0580:37 codes | Sanfilippo mucopolysaccharidoses |
| E7629 | CC | 0580:37 codes | Other mucopolysaccharidoses |
| E763 | CC | 0580:37 codes | Mucopolysaccharidosis, unspecified |
| E768 | CC | 0580:37 codes | Other disorders of glucosaminoglycan metabolism |
| E769 | CC | 0580:37 codes | Glucosaminoglycan metabolism disorder, unspecified |
| E7871 | CC | 0581:41 codes | Barth syndrome |
| E7872 | CC | 0581:41 codes | Smith-Lemli-Opitz syndrome |
| E791 | CC | 0525:35 codes | Lesch-Nyhan syndrome |
| E792 | CC | 0525:35 codes | Myoadenylate deaminase deficiency |
| E7981 | CC | 0525:35 codes | Aicardi-Goutieres syndrome |
| E7982 | CC | 0525:35 codes | Hereditary xanthinuria |
| E7989 | CC | 0525:35 codes | Other specified disorders of purine and pyrimidine metabolism |
| E799 | CC | 0525:35 codes | Disorder of purine and pyrimidine metabolism, unspecified |
| E800 | CC | 0525:35 codes | Hereditary erythropoietic porphyria |
| E801 | CC | 0525:35 codes | Porphyria cutanea tarda |
| E8020 | CC | 0525:35 codes | Unspecified porphyria |
| E8021 | CC | 0525:35 codes | Acute intermittent (hepatic) porphyria |
| E8029 | CC | 0525:35 codes | Other porphyria |
| E803 | CC | 0582:41 codes | Defects of catalase and peroxidase |
| E83820 | CC | 0583:4 codes | Generalized arterial calcification of infancy with unspecified genetic causality |
| E83821 | CC | 0583:4 codes | ENPP1 deficiency causing generalized arterial calcification of infancy |
| E83823 | CC | 0583:4 codes | ABCC6 deficiency causing generalized arterial calcification of infancy |
| E83825 | CC | 0583:4 codes | CD73 deficiency causing arterial calcification |
| E840 | MCC | 0584:5 codes | Cystic fibrosis with pulmonary manifestations |
| E8411 | MCC | 0584:5 codes | Meconium ileus in cystic fibrosis |
| E8419 | CC | 0584:5 codes | Cystic fibrosis with other intestinal manifestations |
| E848 | CC | 0584:5 codes | Cystic fibrosis with other manifestations |
| E849 | CC | 0584:5 codes | Cystic fibrosis, unspecified |
| E850 | CC | 0585:10 codes | Non-neuropathic heredofamilial amyloidosis |
| E851 | CC | 0585:10 codes | Neuropathic heredofamilial amyloidosis |
| E852 | CC | 0585:10 codes | Heredofamilial amyloidosis, unspecified |
| E853 | CC | 0585:10 codes | Secondary systemic amyloidosis |
| E854 | CC | 0585:10 codes | Organ-limited amyloidosis |
| E8581 | CC | 0585:10 codes | Light chain (AL) amyloidosis |
| E8582 | CC | 0585:10 codes | Wild-type transthyretin-related (ATTR) amyloidosis |
| E8589 | CC | 0585:10 codes | Other amyloidosis |
| E859 | CC | 0585:10 codes | Amyloidosis, unspecified |
| E870 | CC | 0586:17 codes | Hyperosmolality and hypernatremia |
| E871 | CC | 0586:17 codes | Hypo-osmolality and hyponatremia |
| E8720 | CC | 0586:17 codes | Acidosis, unspecified |
| E8721 | CC | 0586:17 codes | Acute metabolic acidosis |
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Centers for Medicare & Medicaid Services, 7500 Security Boulevard Baltimore, MD 21244 12 Mar 2025 12:04:04 CMS, code-revision=373, description-revision=1431 |